Diffuse large B-cell lymphoma with chronic inflammation
Synonyms: DLBCL with chronic inflammation
- Type
- Disease
- Group
- Disorder
- Status
- active
Diffuse large B-cell lymphoma with chronic inflammation is an Epstein-Barr virus-associated malignant lymphoproliferative disorder, developing in a context of long-standing or slow-growing, chronically inflamed lesions, such as chronic pyothorax, metallic implants in bones and joints, chronic osteomyelitis, chronic venous ulcer, or, rarely granulomatous inflammation. The tumor is usually primarily localized, with no involvement of other organs.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Diffuse large B-cell lymphoma with chronic inflammation | DLBCL with chronic inflammation |
| fr | Lymphome diffus à grandes cellules B avec inflammation chronique | DLBCL avec inflammation chronique |
| de | B-Zell-Lymphom, diffuses großzelliges, mit chronischer Entzündung | DLBCL bei chronischer Entzündung |
| es | Linfoma difuso de células B grandes con inflamación crónica | DLBCL con inflamación crónica · LDCBG con inflamación crónica |
| it | Linfoma diffuso a grandi cellule B con infiammazione cronica | DLBCL con infiammazione cronica |
| nl | Diffuus grootcellig B-cellymfoom met chronische ontsteking | DLBCL met chronische ontsteking |
| pt | Linfoma difuso de células B grandes com inflamação crónica | |
| pl | Chłoniak rozlany z dużych komórek B z przewlekłym zapaleniem | DLBCL z przewlekłym zapaleniem |
| cs | Difuzní velkobuněčný B-lymfom s chronickým zánětem | DLBCL s chronickým zánětem |
| uk | Дифузна велика В-клітинна лімфома з хронічним запаленням | DLBCL з хронічним запаленням |
| zh | 慢性炎症相关弥漫大B细胞淋巴瘤 | 慢性炎症相关弥漫大B细胞淋巴瘤 |
| tr | Kronik iltihap ile seyreden diffüz büyük B-hücreli lenfoma | Kronik iltihaplı DLBCL |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | C83.3 | NTBT | attributed | validated |
| MONDO | 0017601 | E | validated | |
| UMLS | C4511460 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (2):
- ORPHA:544Diffuse large B-cell lymphoma
rare hematological diseases; rare neoplastic diseases; rare transplant-related disorders - ORPHA:289644Epstein-Barr virus-associated malignant lymphoproliferative disorder
rare neoplastic diseases
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
0 recordsNo prevalence record in this release.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/300888
- This record as JSON: /data/d/300888.json