ORPHA:289644
Epstein-Barr virus-associated malignant lymphoproliferative disorder
Synonyms: EBV-associated lymphoproliferative disorder
- Type
- Category
- Group
- Group of disorders
- Status
- active
This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.
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Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Epstein-Barr virus-associated malignant lymphoproliferative disorder | EBV-associated lymphoproliferative disorder |
| fr | Syndrome lymphoprolifératif malin associé au virus Epstein-Barr | Syndrome lymphoprolifératif associé à l'EBV |
| de | Epstein-Barr Virus-assoziierte lymphoproliferative Krankheit | Lymphoproliferative Krankheit, EBV-assoziierte |
| es | Trastorno linfoproliferativo maligno asociado al virus de Epstein-Barr | Trastorno linfoproliferativo asociado al EBV |
| it | Malattia linfoproliferativa maligna associata al virus di Epstein-Barr | Malattia linfoproliferativa associata a EBV |
| nl | Epstein-Barrvirus-geassocieerde maligne lymfoproliferatieve stoornis | EBV-geassocieerde lymfoproliferatieve stoornis · Epstein-Barrvirus-geassocieerde kwaadaardige lymfoproliferatieve stoornis |
| pt | Doença linfoproliferativa associada a vírus Epstein-Barr | Doença linfoproliferativa associada a EBV |
| pl | Choroba limfoproliferacyjna związana z wirusem Epsteina i Barra | Choroba limfoproliferacyjna związana z EBV |
| cs | Maligní lymfoproliferativní onemocnění asociovaná s virem Epsteina-Barrové | Lymfoproliferativní onemocnění asociovaná s virem Epsteina-Barrové · Maligní lymfoproliferativní onemocnění asociovaná s virem Epstein-Barrové · Lymfoproliferativní onemocnění asociovaná s virem Epstein-Barrové |
| uk | Злоякісне лімфопроліферативне захворювання, асоційоване з вірусом Епштейн-Барр | ЕБВ-асоційований лімфопроліферативний розлад |
| zh | EB病毒相关恶性淋巴增生性疾病 | EB病毒相关恶性淋巴增生性疾病 |
| tr | Epstein-Barr virüsü-ilişkili habis lenfoproliferatif bozuklu | EBV-ilişkili lenfoproliferatif bozukluk |
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Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| MONDO | 0017343 | E | validated | |
| MONDO | 17343 | E | validated | |
| UMLS | C2363744 | E | validated | |
| MedDRA | 10068349 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
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Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:289638Epstein-Barr Virus-related tumor
rare neoplastic diseases
Children (12):
- ORPHA:543Burkitt lymphoma
- ORPHA:300888Diffuse large B-cell lymphoma with chronic inflammation
- ORPHA:289661Epstein-Barr virus-positive diffuse large B-cell lymphoma
- ORPHA:86879Extranodal nasal NK/T cell lymphoma
- ORPHA:98293Hodgkin lymphoma
- ORPHA:364039Hydroa vacciniforme-like lymphoma
- ORPHA:86869Lymphomatoid granulomatosis
- ORPHA:289666Plasmablastic lymphoma
- ORPHA:70568Post-transplant lymphoproliferative disease
- ORPHA:46135Primary central nervous system lymphoma
- ORPHA:48686Primary effusion lymphoma
- ORPHA:364033Systemic Epstein-Barr virus-positive T-cell lymphoproliferative disease of childhood
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Genes
0 directOrphanet records no gene directly on this code.
5
Prevalence and incidence
0 recordsNo prevalence record in this release.
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HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
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Sources for this card
- Orphanet page: orpha.net/en/disease/detail/289644
- This record as JSON: /data/d/289644.json