ORPHA:280369
Rare pediatric vasculitis
- Type
- Category
- Group
- Group of disorders
- Status
- active
This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.
1
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Rare pediatric vasculitis | |
| fr | Vascularite rare de l'enfant | |
| de | Seltene Vaskulitis des Kindes | |
| es | Vasculitis pediátrica rara | |
| it | Vasculite pediatrica | |
| nl | Zeldzame pediatrische vasculitis | |
| pt | Vasculite pediátrica rara | |
| pl | Rzadkie dziecięce zapalenie naczyń | |
| cs | Vaskulitidy v pediatrii | Vzácné vaskulitidy v pediatrii |
| uk | Рідкісні дитячі васкуліти | |
| zh | 罕见小儿血管炎 | |
| tr | Nadir pediatrik vaskülit |
2
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| UMLS | C5680782 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
3
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:280342Rare systemic or rheumatological disease of childhood
rare systemic or rheumatologic diseases of childhood
Children (12):
- ORPHA:156152Anti-neutrophil cytoplasmic antibody-associated vasculitis
- ORPHA:1467Cogan syndrome
- ORPHA:91138Cryoglobulinemic vasculitis
- ORPHA:404553Deficiency of adenosine deaminase 2
- ORPHA:36412Hypocomplementemic urticarial vasculitis
- ORPHA:761Immunoglobulin A vasculitis
- ORPHA:2331Kawasaki disease
- ORPHA:767Polyarteritis nodosa
- ORPHA:425120STING-associated vasculopathy with onset in infancy
- ORPHA:445197Secondary vasculitis
- ORPHA:3287Takayasu arteritis
- ORPHA:251328Unclassified vasculitis
4
Genes
0 directOrphanet records no gene directly on this code.
5
Prevalence and incidence
0 recordsNo prevalence record in this release.
6
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
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Sources for this card
- Orphanet page: orpha.net/en/disease/detail/280369
- This record as JSON: /data/d/280369.json