ORPHA:251328
Unclassified vasculitis
- Type
- Disease
- Group
- Disorder
- Inheritance
- Not applicable
- Status
- active
A rare vasculitis characterized by an inflammatory disease of blood vessels which cannot be assigned to any of the known categories of vasculitis. Clinical features are highly variable, depending on the nature and extent of the inflammatory process, as well as the type of vessels and organ systems involved.
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Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Unclassified vasculitis | |
| fr | Vascularite non classifiée | |
| de | Vaskulitis, unklassifizierte | |
| es | Vasculitis no clasificada | |
| it | Vasculite non classificata | |
| nl | Niet-geclassificeerde vasculitis | |
| pt | Vasculite não-classificada | |
| pl | Niesklasyfikowane zapalenie naczyń | |
| cs | Neklasifikovaná vaskulitida | |
| uk | Некласифікований васкуліт | |
| zh | 未分类血管炎 | |
| tr | Sınıflandırılmamış vaskülit |
Definition in:
2
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | I77.6 | NTBT | attributed | validated |
| ICD-11 | 4A44.Y | NTBT | attributed | validated |
| MONDO | 0016665 | E | validated | |
| UMLS | C5680712 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
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Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (2):
- ORPHA:280369Rare pediatric vasculitis
rare systemic or rheumatologic diseases of childhood - ORPHA:52759Vasculitis
rare systemic and rheumatological diseases; rare circulatory system diseases
No children.
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Genes
0 directOrphanet records no gene directly on this code.
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Prevalence and incidence
0 recordsNo prevalence record in this release.
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HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
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Sources for this card
- Orphanet page: orpha.net/en/disease/detail/251328
- This record as JSON: /data/d/251328.json