ORPHA:280315
Autoimmune pancreatitis type 2
Synonyms: AIP type 2 · Duct-centric pancreatitis
- Type
- Disease
- Group
- Disorder
- Inheritance
- Not applicable
- Age of onset
- Adult
- Status
- active
Type 2 autoimmune pancreatitis is a form of autoimmune pancreatitis affecting both sexes and having a younger age of onset (<60 years) and presenting with abdominal pain, steatorrhea and obstructive jaundice.
1
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Autoimmune pancreatitis type 2 | AIP type 2 · Duct-centric pancreatitis |
| fr | Pancréatite auto-immune type 2 | AIP type 2 · Pancréatite centro-canalaire |
| de | Pankreatitis, autoimmune, Typ 2 | AIP Typ 2 · Autoimmun-Pankreatitis Typ 2 · Pankreatitis, gangzentrierte |
| es | Pancreatitis autoinmune tipo 2 | AIP tipo 2 · Pancreatitis ducto-céntrica |
| it | Pancreatite autoimmune, tipo 2 | AIP, tipo 2 · Pancreatite dottocentrica |
| nl | Auto-immune pancreatitis type 2 | AIP type 2 · Kanaal-centrische pancreatitis |
| pt | Pancreatite autoimune tipo 2 | PAI tipo 2 · Pancreatite ducto-cêntrica |
| pl | Autoimmunologiczne zapalenie trzustki typu 2 | AIP typu 2 · Zapalenie trzustki z centrycznym zajęciem przewodu trzustkowego |
| cs | Autoimunitní pankreatitida, typ 2 | AIP typ 2 · Centroduktální pankreatitida |
| uk | Аутоімунний панкреатит, тип 2 | AIP тип 2 · Протокоцентричний панкреатит |
| zh | 自身免疫性胰腺炎2型 | Duct-centric胰腺炎 |
| tr | Otoimmün pankreatit tip 2 | AIP tip 2 · Kanal-merkezli pankreatit |
Definition in:
2
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | K86.1 | NTBT | attributed | validated |
| ICD-11 | DC33 | NTBT | index | validated |
| MONDO | 0017228 | E | validated | |
| UMLS | C5197785 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
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Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:103919Autoimmune pancreatitis
rare gastroenterological diseases
No children.
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Genes
0 directOrphanet records no gene directly on this code.
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Prevalence and incidence
1 record| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Point prevalence | 1-9 / 1 000 000 | 0.5 / 100 000 | Worldwide | Value and class | Validated | 34670874[PMID]_ORPHANET |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
6
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
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Sources for this card
- Orphanet page: orpha.net/en/disease/detail/280315
- This record as JSON: /data/d/280315.json