Autoimmune pancreatitis
Synonyms: AIP
- Type
- Clinical group
- Group
- Group of disorders
- Inheritance
- Not applicable
- Status
- active
A rare pancreatic disease characterized by chronic non-alcoholic pancreatitis that presents with abdominal pain, steatorrhea, obstructive jaundice and responds well to steroid therapy and is seen in two subforms: type 1, which affects elderly males, involves other organs and has increased immunoglobin G4 (IgG4) levels and type 2, which affects both sexes equally but presents at a younger age and has no other organ involvement or increased IgG4 levels.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Autoimmune pancreatitis | AIP |
| fr | Pancréatite auto-immune | = en |
| de | Pankreatitis, autoimmune | Autoimmun-Pankreatitis |
| es | Pancreatitis autoinmune | = en |
| it | Pancreatite autoimmune | = en |
| nl | Auto-immune pancreatitis | AIP · Auto-immune alvleesklierontsteking |
| pt | Pancreatite autoimune | |
| pl | Autoimmunologiczne zapalenie trzustki | = en |
| cs | Autoimunitní pankreatitida | = en |
| uk | Аутоімунний панкреатит | = en |
| zh | 自身免疫性胰腺炎 | = en |
| tr | Otoimmün pankreatit | = en |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-11 | DC33 | E | specific | validated |
| MONDO | 0015175 | E | validated | |
| MONDO | 15175 | E | validated | |
| MeSH | D000081012 | E | validated | |
| UMLS | C2609129 | E | validated | |
| GARD | 10911 | E | validated | |
| MedDRA | 10069002 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:101937Rare pancreatic disease
rare gastroenterological diseases
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
0 recordsNo prevalence record in this release.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/103919
- This record as JSON: /data/d/103919.json