{"orpha":280315,"name":"Autoimmune pancreatitis type 2","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":["AIP type 2","Duct-centric pancreatitis"],"definition":"Type 2 autoimmune pancreatitis is a form of autoimmune pancreatitis affecting both sexes and having a younger age of onset (<60 years) and presenting with abdominal pain, steatorrhea and obstructive jaundice.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-280315/","orphanet_url":"https://www.orpha.net/en/disease/detail/280315","names":{"fr":{"name":"Pancréatite auto-immune type 2","synonyms":["AIP type 2","Pancréatite centro-canalaire"],"definition":"La pancréatite auto-immune de type 2 est une forme de pancréatite auto-immune affectant les 2 sexes et se manifestant avant les 60 ans par une douleur abdominale, une stéatorrhée et un ictère obstructif."},"de":{"name":"Pankreatitis, autoimmune, Typ 2","synonyms":["AIP Typ 2","Autoimmun-Pankreatitis Typ 2","Pankreatitis, gangzentrierte"],"definition":"Der Typ 2 der Autoimmun-Pankreatitis, eine Unterform der Autoimmun-Pankreatitis (s. dort), tritt in beiden Geschlechtern auf, hat ein früheres Erkrankungsalter (< 60 Jahre) und manifestiert sich mit Leibschmerzen, Steatorrhoe und obstruktivem Ikterus."},"es":{"name":"Pancreatitis autoinmune tipo 2","synonyms":["AIP tipo 2","Pancreatitis ducto-céntrica"],"definition":"La pancreatitis autoinmune tipo 2 es una forma de pancreatitis autoinmune (consulte este término) que afecta a ambos sexos y que tiene una edad de aparición más temprana que la tipo 1 (<60 años); se presenta con dolor abdominal, esteatorrea e ictericia obstructiva."},"it":{"name":"Pancreatite autoimmune, tipo 2","synonyms":["AIP, tipo 2","Pancreatite dottocentrica"],"definition":"La pancreatite autoimmune tipo 2 è una forma di pancreatite autoimmune (si veda questo termine), che colpisce entrambi i sessi ed esordisce a un'età più giovane (< 60 anni). Si manifesta con dolore addominale, steatorrea e ittero ostruttivo."},"nl":{"name":"Auto-immune pancreatitis type 2","synonyms":["AIP type 2","Kanaal-centrische pancreatitis"],"definition":"Een vorm van auto-immune pancreatitis die beide geslachten treft, een jongere aanvangsleeftijd vertoont (jonger dan 60 jaar), en gekenmerkt wordt door abdominale pijn, steatorroe, en obstructieve geelzucht."},"pt":{"name":"Pancreatite autoimune tipo 2","synonyms":["PAI tipo 2","Pancreatite ducto-cêntrica"]},"pl":{"name":"Autoimmunologiczne zapalenie trzustki typu 2","synonyms":["AIP typu 2","Zapalenie trzustki z centrycznym zajęciem przewodu trzustkowego"]},"cs":{"name":"Autoimunitní pankreatitida, typ 2","synonyms":["AIP typ 2","Centroduktální pankreatitida"]},"uk":{"name":"Аутоімунний панкреатит, тип 2","synonyms":["AIP тип 2","Протокоцентричний панкреатит"],"definition":"Type 2 autoimmune pancreatitis is a form of autoimmune pancreatitis (see this term) affecting both sexes and having a younger age of onset (<60 years) and presenting with abdominal pain, steatorrhea and obstructive jaundice."},"zh":{"name":"自身免疫性胰腺炎2型","synonyms":["Duct-centric胰腺炎"],"definition":"自身免疫性胰腺炎2型是一种自身免疫性胰腺炎（见本术语），男女均受影响，发病年龄较小（ sup 60岁），表现为腹痛、脂肪泻和梗阻性黄疸。"},"tr":{"name":"Otoimmün pankreatit tip 2","synonyms":["AIP tip 2","Kanal-merkezli pankreatit"]}},"xrefs":[{"source":"ICD-10","code":"K86.1","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"DC33","qualifier":"NTBT","icd_relation":"index","validated":true,"icd11_uri":"319563521"},{"source":"MONDO","code":"0017228","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C5197785","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":97935,"name":"Rare gastroenterologic disease"},"parents":[{"orpha":103919,"name":"Autoimmune pancreatitis","classifications":[152]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":["Adult"],"prevalence":[{"type":"Point prevalence","qualification":"Value and class","class":"1-9 / 1 000 000","value":0.5,"area":"Worldwide","status":"Validated","source":"34670874[PMID]_ORPHANET"}],"phenotypes":null}