ORPHA:264935
Primary interstitial lung disease in childhood and adulthood due to alveolar vascular disorder
Synonyms: Primary ILD in childhood and adulthood due to alveolar vascular disorder
- Type
- Category
- Group
- Group of disorders
- Status
- active
This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.
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Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Primary interstitial lung disease in childhood and adulthood due to alveolar vascular disorder | Primary ILD in childhood and adulthood due to alveolar vascular disorder |
| fr | Pneumopathie interstitielle primaire de l'enfant et de l'adulte due à une anomalie vasculaire des alvéoles | ILD primaire de l'enfant et de l'adulte due à une anomalie vasculaire des alvéoles |
| de | Interstitielle Lungenkrankheit, primäre, des Kindes/Erwachsenen durch alveoläre Vaskulationsstörungen | Primary ILD des Kindes/Erwachsenen durch alveoläre Vaskulationsstörungen |
| es | Enfermedad pulmonar intersticial primaria de la infancia y del adulto por un trastorno vascular alveolar | EPI primaria de la infancia y del adulto por un trastorno vascular alveolar |
| it | Pneumopatia interstiziale primitiva dell'infanzia e dell'età adulta da anomalia vascolare degli alveoli | ILD primitiva dell'infanzia e dell'età adulta da anomalia vascolare degli alveoli |
| nl | Primaire interstitiële longziekte in de kinderjaren en volwassenheid door een alveolaire vasculaire stoornis | Primaire ILD in de kinderjaren en volwassenheid door een alveolaire vasculaire stoornis |
| pt | Doença pulmonar intersticial primária da infância e do adulto por alteração vascular alveolar | |
| pl | Pierwotna choroba śródmiąższowa płuc wieku dziecięcego i dorosłego z powodu zaburzeń naczyniowych pęcherzyków płucnych | Pierwotna ILD wieku dziecięcego i dorosłego z powodu zaburzeń naczyniowych pęcherzyków płucnych |
| cs | Primární intersticiální plicní nemoc v dětství a dospělosti způsobená alveolární vaskulární poruchou | Primární ILD v dětství a dospělosti způsobená alveolární vaskulární poruchou |
| uk | Первинне інтерстиціальне захворювання легень у дитячому та дорослому віці, зумовлене альвеолярним судинним синдромом | Первинна ILD у дитячому та дорослому віці внаслідок альвеолярного судинного захворювання |
| zh | 肺泡血管疾病所致儿童期和成年期原发性间质性肺病 | 肺泡血管疾病所致儿童期和成年期原发性ILD |
| tr | Alveolar vasküler bozukluğa bağlı çocukluk ve yetişkinlik dönemi primer interstisyel akciğer hastalığı | Alveolar vasküler bozukluğa bağlı çocukluk ve erişkinlikte primer ILD |
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Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| MONDO | 17033 | E | validated | |
| UMLS | C5679749 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
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Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:264762Primary interstitial lung disease in childhood and adulthood
rare respiratory diseases; rare transplant-related disorders
Children (1):
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Genes
0 directOrphanet records no gene directly on this code.
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Prevalence and incidence
0 recordsNo prevalence record in this release.
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HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
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Sources for this card
- Orphanet page: orpha.net/en/disease/detail/264935
- This record as JSON: /data/d/264935.json