{"orpha":264935,"name":"Primary interstitial lung disease in childhood and adulthood due to alveolar vascular disorder","type":"Category","group":"Group of disorders","status":"active","flags":[],"synonyms":["Primary ILD in childhood and adulthood due to alveolar vascular disorder"],"definition":null,"note":"This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.","url":"https://raremap.alftech.space/d/ORPHA-264935/","orphanet_url":"https://www.orpha.net/en/disease/detail/264935","names":{"fr":{"name":"Pneumopathie interstitielle primaire de l'enfant et de l'adulte due à une anomalie vasculaire des alvéoles","synonyms":["ILD primaire de l'enfant et de l'adulte due à une anomalie vasculaire des alvéoles"]},"de":{"name":"Interstitielle Lungenkrankheit, primäre, des Kindes/Erwachsenen durch alveoläre Vaskulationsstörungen","synonyms":["Primary ILD des Kindes/Erwachsenen durch alveoläre Vaskulationsstörungen"]},"es":{"name":"Enfermedad pulmonar intersticial primaria de la infancia y del adulto por un trastorno vascular alveolar","synonyms":["EPI primaria de la infancia y del adulto por un trastorno vascular alveolar"]},"it":{"name":"Pneumopatia interstiziale primitiva dell'infanzia e dell'età adulta da anomalia vascolare degli alveoli","synonyms":["ILD primitiva dell'infanzia e dell'età adulta da anomalia vascolare degli alveoli"]},"nl":{"name":"Primaire interstitiële longziekte in de kinderjaren en volwassenheid door een alveolaire vasculaire stoornis","synonyms":["Primaire ILD in de kinderjaren en volwassenheid door een alveolaire vasculaire stoornis"]},"pt":{"name":"Doença pulmonar intersticial primária da infância e do adulto por alteração vascular alveolar"},"pl":{"name":"Pierwotna choroba śródmiąższowa płuc wieku dziecięcego i dorosłego z powodu zaburzeń naczyniowych pęcherzyków płucnych","synonyms":["Pierwotna ILD wieku dziecięcego i dorosłego z powodu zaburzeń naczyniowych pęcherzyków płucnych"]},"cs":{"name":"Primární intersticiální plicní nemoc v dětství a dospělosti způsobená alveolární vaskulární poruchou","synonyms":["Primární ILD v dětství a dospělosti způsobená alveolární vaskulární poruchou"]},"uk":{"name":"Первинне інтерстиціальне захворювання легень у дитячому та дорослому віці, зумовлене альвеолярним судинним синдромом","synonyms":["Первинна ILD у дитячому та дорослому віці внаслідок альвеолярного судинного захворювання"]},"zh":{"name":"肺泡血管疾病所致儿童期和成年期原发性间质性肺病","synonyms":["肺泡血管疾病所致儿童期和成年期原发性ILD"]},"tr":{"name":"Alveolar vasküler bozukluğa bağlı çocukluk ve yetişkinlik dönemi primer interstisyel akciğer hastalığı","synonyms":["Alveolar vasküler bozukluğa bağlı çocukluk ve erişkinlikte primer ILD"]}},"xrefs":[{"source":"MONDO","code":"17033","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C5679749","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":97955,"name":"Rare respiratory disease"},"parents":[{"orpha":264762,"name":"Primary interstitial lung disease in childhood and adulthood","classifications":[184,233]}],"children":[{"orpha":182101,"name":"Idiopathic eosinophilic pneumonia","type":"Clinical group"}],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":[],"prevalence":[],"phenotypes":null}