ORPHA:264762
Primary interstitial lung disease in childhood and adulthood
Synonyms: Primary ILD in childhood and adulthood
- Type
- Category
- Group
- Group of disorders
- Status
- active
This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.
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Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Primary interstitial lung disease in childhood and adulthood | Primary ILD in childhood and adulthood |
| fr | Pneumopathie interstitielle primaire de l'enfance et de l'adulte | ILD primaire de l'enfance et de l'adulte |
| de | Interstitielle Lungenkrankheit, primäre, des Kindes/Erwachsenen | Primäre ILD des Kindes/Erwachsenen |
| es | Enfermedad pulmonar intersticial primaria de la infancia y del adulto | EPI primaria de la infancia y del adulto |
| it | Pneumopatia interstiziale primitiva dell'infanzia e dell'età adulta | ILD primitiva dell'infanzia e dell'età adulta |
| nl | Primaire interstitiële longziekte in de kinderjaren en volwassenheid | Primaire ILD in de kinderjaren en volwassenheid |
| pt | Doença pulmonar intersticial primária da infância e do adulto | |
| pl | Pierwotna choroba śródmiąższowa płuc wieku dziecięcego i dorosłego | Pierwotna ILD wieku dziecięcego i dorosłego |
| cs | Primární intersticiální plicní nemoc v dětství a dospělosti | Primární ILD v dětství a dospělosti |
| uk | Первинне інтерстиціальне захворювання легень у дитячому та дорослому віці | Первинна ILD у дитячому та дорослому віці |
| zh | 儿童期和成年期原发性间质性肺病 | 儿童期和成年期原发性ILD |
| tr | Çocukluk ve yetişkinlik dönemi primer interstisyel akciğer hastalığı | Çocukluk ve erişkinlikte primer ILD |
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Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| MONDO | 17031 | E | validated | |
| UMLS | C5679747 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
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Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:264757Interstitial lung disease in childhood and adulthood
rare respiratory diseases; rare transplant-related disorders
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Genes
0 directOrphanet records no gene directly on this code.
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Prevalence and incidence
0 recordsNo prevalence record in this release.
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HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
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Sources for this card
- Orphanet page: orpha.net/en/disease/detail/264762
- This record as JSON: /data/d/264762.json