raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:264762

Primary interstitial lung disease in childhood and adulthood

Synonyms: Primary ILD in childhood and adulthood

Type
Category
Group
Group of disorders
Status
active

This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enPrimary interstitial lung disease in childhood and adulthoodPrimary ILD in childhood and adulthood
frPneumopathie interstitielle primaire de l'enfance et de l'adulteILD primaire de l'enfance et de l'adulte
deInterstitielle Lungenkrankheit, primäre, des Kindes/ErwachsenenPrimäre ILD des Kindes/Erwachsenen
esEnfermedad pulmonar intersticial primaria de la infancia y del adultoEPI primaria de la infancia y del adulto
itPneumopatia interstiziale primitiva dell'infanzia e dell'età adultaILD primitiva dell'infanzia e dell'età adulta
nlPrimaire interstitiële longziekte in de kinderjaren en volwassenheidPrimaire ILD in de kinderjaren en volwassenheid
ptDoença pulmonar intersticial primária da infância e do adulto
plPierwotna choroba śródmiąższowa płuc wieku dziecięcego i dorosłegoPierwotna ILD wieku dziecięcego i dorosłego
csPrimární intersticiální plicní nemoc v dětství a dospělostiPrimární ILD v dětství a dospělosti
ukПервинне інтерстиціальне захворювання легень у дитячому та дорослому віціПервинна ILD у дитячому та дорослому віці
zh儿童期和成年期原发性间质性肺病儿童期和成年期原发性ILD
trÇocukluk ve yetişkinlik dönemi primer interstisyel akciğer hastalığıÇocukluk ve erişkinlikte primer ILD
2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
MONDO17031Evalidated
UMLSC5679747Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

Children (3):

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card