{"orpha":264762,"name":"Primary interstitial lung disease in childhood and adulthood","type":"Category","group":"Group of disorders","status":"active","flags":[],"synonyms":["Primary ILD in childhood and adulthood"],"definition":null,"note":"This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.","url":"https://raremap.alftech.space/d/ORPHA-264762/","orphanet_url":"https://www.orpha.net/en/disease/detail/264762","names":{"fr":{"name":"Pneumopathie interstitielle primaire de l'enfance et de l'adulte","synonyms":["ILD primaire de l'enfance et de l'adulte"]},"de":{"name":"Interstitielle Lungenkrankheit, primäre, des Kindes/Erwachsenen","synonyms":["Primäre ILD des Kindes/Erwachsenen"]},"es":{"name":"Enfermedad pulmonar intersticial primaria de la infancia y del adulto","synonyms":["EPI primaria de la infancia y del adulto"]},"it":{"name":"Pneumopatia interstiziale primitiva dell'infanzia e dell'età adulta","synonyms":["ILD primitiva dell'infanzia e dell'età adulta"]},"nl":{"name":"Primaire interstitiële longziekte in de kinderjaren en volwassenheid","synonyms":["Primaire ILD in de kinderjaren en volwassenheid"]},"pt":{"name":"Doença pulmonar intersticial primária da infância e do adulto"},"pl":{"name":"Pierwotna choroba śródmiąższowa płuc wieku dziecięcego i dorosłego","synonyms":["Pierwotna ILD wieku dziecięcego i dorosłego"]},"cs":{"name":"Primární intersticiální plicní nemoc v dětství a dospělosti","synonyms":["Primární ILD v dětství a dospělosti"]},"uk":{"name":"Первинне інтерстиціальне захворювання легень у дитячому та дорослому віці","synonyms":["Первинна ILD у дитячому та дорослому віці"]},"zh":{"name":"儿童期和成年期原发性间质性肺病","synonyms":["儿童期和成年期原发性ILD"]},"tr":{"name":"Çocukluk ve yetişkinlik dönemi primer interstisyel akciğer hastalığı","synonyms":["Çocukluk ve erişkinlikte primer ILD"]}},"xrefs":[{"source":"MONDO","code":"17031","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C5679747","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":97955,"name":"Rare respiratory disease"},"parents":[{"orpha":264757,"name":"Interstitial lung disease in childhood and adulthood","classifications":[184,233]}],"children":[{"orpha":99931,"name":"Idiopathic pulmonary hemosiderosis","type":"Disease"},{"orpha":264930,"name":"Primary interstitial lung disease in childhood and adulthood due to alveolar structure disorder","type":"Category"},{"orpha":264935,"name":"Primary interstitial lung disease in childhood and adulthood due to alveolar vascular disorder","type":"Category"}],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":[],"prevalence":[],"phenotypes":null}