ORPHA:264740
Primary interstitial lung disease specific to adulthood
Synonyms: Primary ILD specific to adulthood
- Type
- Category
- Group
- Group of disorders
- Status
- active
This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.
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Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Primary interstitial lung disease specific to adulthood | Primary ILD specific to adulthood |
| fr | Pneumopathie interstitielle primaire spécifique de l'adulte | ILD primaire spécifique de l'adulte |
| de | Primäre interstitielle Lungenkrankheit des Erwachsenen | Primäre ILD des Erwachsenen |
| es | Enfermedad pulmonar intersticial primaria específica del adulto | EPI primaria específica del adulto |
| it | Pneumopatia interstiziale primitiva specifica dell'età adulta | ILD primitiva specifica dell'età adulta |
| nl | Primaire interstitiële longziekte specifiek voor de volwassenheid | Primaire ILD specifiek voor de volwassenheid |
| pt | Doença pulmonar intersticial primária específica do adulto | |
| pl | Pierwotna śródmiąższowa choroba płuc specyficzna dla wieku dorosłego | Pierwotna ILD specyficzna dla wieku dorosłego |
| cs | Primární intersticiální plicní nemoc specifická pro dospělé | Primární ILD specifická pro dospělé |
| uk | Первинне інтерстиціальне захворювання легень, характерне для дорослого віку | Первинна ILD, специфічна для дорослого віку |
| zh | 成年期特有的原发性间质性肺病 | 成年期特有的原发性ILD |
| tr | Yetişkinlik çağı primer interstisyel akciğer hastalığı | Erişkinliğe özgü primer ILD |
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Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| MONDO | 17027 | E | validated | |
| UMLS | C5679744 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
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Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:264735Interstitial lung disease specific to adulthood
rare respiratory diseases; rare transplant-related disorders
Children (8):
- ORPHA:70578Adult acute respiratory distress syndrome
- ORPHA:747Autoimmune pulmonary alveolar proteinosis
- ORPHA:122Birt-Hogg-Dubé syndrome
- ORPHA:221043Hereditary fibrosing poikiloderma-tendon contractures-myopathy-pulmonary fibrosis syndrome
- ORPHA:98300Idiopathic interstitial pneumonia
- ORPHA:538Lymphangioleiomyomatosis
- ORPHA:182098Pneumoconiosis
- ORPHA:210136Pulmonary fibrosis-hepatic hyperplasia-bone marrow hypoplasia syndrome
4
Genes
0 directOrphanet records no gene directly on this code.
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Prevalence and incidence
0 recordsNo prevalence record in this release.
6
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
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Sources for this card
- Orphanet page: orpha.net/en/disease/detail/264740
- This record as JSON: /data/d/264740.json