{"orpha":264740,"name":"Primary interstitial lung disease specific to adulthood","type":"Category","group":"Group of disorders","status":"active","flags":[],"synonyms":["Primary ILD specific to adulthood"],"definition":null,"note":"This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.","url":"https://raremap.alftech.space/d/ORPHA-264740/","orphanet_url":"https://www.orpha.net/en/disease/detail/264740","names":{"fr":{"name":"Pneumopathie interstitielle primaire spécifique de l'adulte","synonyms":["ILD primaire spécifique de l'adulte"]},"de":{"name":"Primäre interstitielle Lungenkrankheit des Erwachsenen","synonyms":["Primäre ILD des Erwachsenen"]},"es":{"name":"Enfermedad pulmonar intersticial primaria específica del adulto","synonyms":["EPI primaria específica del adulto"]},"it":{"name":"Pneumopatia interstiziale primitiva specifica dell'età adulta","synonyms":["ILD primitiva specifica dell'età adulta"]},"nl":{"name":"Primaire interstitiële longziekte specifiek voor de volwassenheid","synonyms":["Primaire ILD specifiek voor de volwassenheid"]},"pt":{"name":"Doença pulmonar intersticial primária específica do adulto"},"pl":{"name":"Pierwotna śródmiąższowa choroba płuc specyficzna dla wieku dorosłego","synonyms":["Pierwotna ILD specyficzna dla wieku dorosłego"]},"cs":{"name":"Primární intersticiální plicní nemoc specifická pro dospělé","synonyms":["Primární ILD specifická pro dospělé"]},"uk":{"name":"Первинне інтерстиціальне захворювання легень, характерне для дорослого віку","synonyms":["Первинна ILD, специфічна для дорослого віку"]},"zh":{"name":"成年期特有的原发性间质性肺病","synonyms":["成年期特有的原发性ILD"]},"tr":{"name":"Yetişkinlik çağı primer interstisyel akciğer hastalığı","synonyms":["Erişkinliğe özgü primer ILD"]}},"xrefs":[{"source":"MONDO","code":"17027","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C5679744","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":97955,"name":"Rare respiratory disease"},"parents":[{"orpha":264735,"name":"Interstitial lung disease specific to adulthood","classifications":[184,233]}],"children":[{"orpha":70578,"name":"Adult acute respiratory distress syndrome","type":"Disease"},{"orpha":747,"name":"Autoimmune pulmonary alveolar proteinosis","type":"Disease"},{"orpha":122,"name":"Birt-Hogg-Dubé syndrome","type":"Malformation syndrome"},{"orpha":221043,"name":"Hereditary fibrosing poikiloderma-tendon contractures-myopathy-pulmonary fibrosis syndrome","type":"Disease"},{"orpha":98300,"name":"Idiopathic interstitial pneumonia","type":"Clinical group"},{"orpha":538,"name":"Lymphangioleiomyomatosis","type":"Disease"},{"orpha":182098,"name":"Pneumoconiosis","type":"Clinical group"},{"orpha":210136,"name":"Pulmonary fibrosis-hepatic hyperplasia-bone marrow hypoplasia syndrome","type":"Disease"}],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":[],"prevalence":[],"phenotypes":null}