{"orpha":251328,"name":"Unclassified vasculitis","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":[],"definition":"A rare vasculitis characterized by an inflammatory disease of blood vessels which cannot be assigned to any of the known categories of vasculitis. Clinical features are highly variable, depending on the nature and extent of the inflammatory process, as well as the type of vessels and organ systems involved.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-251328/","orphanet_url":"https://www.orpha.net/en/disease/detail/251328","names":{"fr":{"name":"Vascularite non classifiée","definition":"Vascularite rare, caractérisée par une maladie inflammatoire des vaisseaux sanguins ne rentrant dans aucune catégorie connue de vascularite. Les caractéristiques cliniques varient fortement en fonction de la nature et de l'étendue du processus inflammatoire, ainsi que du type de vaisseaux et de systèmes organiques concernés."},"de":{"name":"Vaskulitis, unklassifizierte","definition":"Eine seltene Vaskulitis, die durch eine entzündliche Erkrankung der Blutgefäße gekennzeichnet ist und sich keiner der bekannten Vaskulitis-Kategorien zuordnen lässt. Die klinischen Merkmale sind sehr unterschiedlich und hängen von der Art und dem Ausmaß des Entzündungsprozesses sowie von der Art der betroffenen Gefäße und Organsysteme ab."},"es":{"name":"Vasculitis no clasificada","definition":"Es una vasculitis poco frecuente caracterizada por enfermedad inflamatoria de los vasos sanguíneos que no puede asignarse a ninguna de las categorías conocidas de vasculitis. Las características clínicas son altamente variables dependiendo de la naturaleza y del alcance del proceso inflamatorio, así como del tipo de vasos y sistemas orgánicos implicados."},"it":{"name":"Vasculite non classificata","definition":"Si tratta di una vasculite rara, caratterizzata da una malattia infiammatoria dei vasi sanguigni che non può essere ricondotta a nessuna delle categorie note di vasculite. I segni clinici sono molto variabili, e dipendono dalla natura e dall'ampiezza del processo infiammatorio, dalla tipologia dei vasi interessati e dagli organi coinvolti."},"nl":{"name":"Niet-geclassificeerde vasculitis","definition":"Een zeldzame vasculitis, gekarakteriseerd door een inflammatoire aandoening van bloedvaten die niet kan toegeschreven worden aan een gekende categorie van vasculitis. Klinische kenmerken zijn zeer variabel, afhankelijk van de aard en de omvang van het inflammatoire proces, alsook van het soort bloedvaten en orgaansystemen die betrokken zijn."},"pt":{"name":"Vasculite não-classificada"},"pl":{"name":"Niesklasyfikowane zapalenie naczyń"},"cs":{"name":"Neklasifikovaná vaskulitida"},"uk":{"name":"Некласифікований васкуліт","definition":"A rare vasculitis characterized by an inflammatory disease of blood vessels which cannot be assigned to any of the known categories of vasculitis. Clinical features are highly variable, depending on the nature and extent of the inflammatory process, as well as the type of vessels and organ systems involved."},"zh":{"name":"未分类血管炎"},"tr":{"name":"Sınıflandırılmamış vaskülit"}},"xrefs":[{"source":"ICD-10","code":"I77.6","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"4A44.Y","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"MONDO","code":"0016665","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C5680712","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":98023,"name":"Rare systemic or rheumatologic disease"},"parents":[{"orpha":280369,"name":"Rare pediatric vasculitis","classifications":[231]},{"orpha":52759,"name":"Vasculitis","classifications":[196,198]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":[],"prevalence":[],"phenotypes":null}