ORPHA:217074
Rare carcinoma of pancreas
Synonyms: Rare pancreatic carcinoma
- Type
- Category
- Group
- Group of disorders
- Inheritance
- Not applicable
- Age of onset
- Adult
- Status
- active
This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.
1
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Rare carcinoma of pancreas | Rare pancreatic carcinoma |
| fr | Carcinome rare du pancréas | |
| de | Seltenes Pankreaskarzinom | Bauchspeicheldrüsenkrebs, seltener |
| es | Carcinoma raro de páncreas | Carcinoma pancreático raro |
| it | Carcinoma raro del pancreas | Cancro pancreatico · Tumore pancreatico |
| nl | Zeldzaam carcinoom van pancreas | Zeldzaam carcinoom van alvleesklier · Zeldzaam pancreatisch carcinoom |
| pt | Carcinoma pancreático | |
| pl | Rzadki rak trzustki | = en |
| cs | Vzácný karcinom pankreatu | Vzácný pankreatický karcinom |
| uk | Рідкісна карцинома підшлункової залози | Рідкісна карцинома підшлункової залози |
| zh | 罕见胰腺癌 | 罕见胰腺癌 |
| tr | Nadir pankreas karsinomu | Nadir pankreas karsinomu |
2
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| MONDO | 16314 | E | validated | |
| MeSH | D010190 | E | validated | |
| UMLS | C5680420 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
3
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:424033Rare epithelial tumor of pancreas
rare gastroenterological diseases; rare neoplastic diseases
Children (8):
- ORPHA:424046Acinar cell carcinoma of pancreas
- ORPHA:1333Familial pancreatic carcinoma
- ORPHA:424058Intraductal papillary mucinous carcinoma of pancreas
- ORPHA:424053Mucinous cystadenocarcinoma of the pancreas
- ORPHA:424065Pancreatic solid pseudopapillary neoplasm
- ORPHA:424073Serous cystadenocarcinoma of pancreas
- ORPHA:424039Squamous cell carcinoma of pancreas
- ORPHA:424080Undifferentiated carcinoma with osteoclast-like giant cells of pancreas
4
Genes
0 directOrphanet records no gene directly on this code.
5
Prevalence and incidence
5 records| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Annual incidence | 1-5 / 10 000 | 11.79 / 100 000 | Europe | Value and class | Validated | RARECARE surveillance of rare cancers in Europe 2011[OTHER] |
| Lifetime Prevalence | 1-9 / 100 000 | 8.3 / 100 000 | Europe | Value and class | Validated | 22033323[PMID]_RARECARE surveillance of rare cancers in Europe[OTHER] |
| Point prevalence | 1-5 / 10 000 | 15.5 / 100 000 | Europe | Value and class | Validated | European Medicines Agency 2013[OTHER]_ORPHANET |
| Annual incidence | 1-9 / 100 000 | 3.9 / 100 000 | Worldwide | Value and class | Validated | World Health Organization 2008[OTHER] |
| Point prevalence | 1-9 / 100 000 | 3.5 / 100 000 | Worldwide | Value and class | Validated | World Health Organization 2008[OTHER] |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
6
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
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Sources for this card
- Orphanet page: orpha.net/en/disease/detail/217074
- This record as JSON: /data/d/217074.json