Serous cystadenocarcinoma of pancreas
Synonyms: Pancreatic serous cystadenocarcinoma
- Type
- Disease
- Group
- Disorder
- Inheritance
- Not applicable
- Age of onset
- Adult
- Status
- active
A very rare, malignant, epithelial tumor of the pancreas composed of cystic structures lined by glycogen-rich clear cells, associated with local invasiveness often involving the spleen, duodenum and/or stomach and metastatic spread to the liver, peritoneum and/or lymph nodes. Presenting symptoms are variable and usually non-specific and include abdominal and/or flank pain, palpable abdominal mass, upper gastrointestinal bleeding, jaundice or abnormal serum liver enzymes, vomiting, anorexia and/or weight loss.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Serous cystadenocarcinoma of pancreas | Pancreatic serous cystadenocarcinoma |
| fr | Cystadénocarcinome séreux du pancréas | Cystadénocarcinome séreux pancréatique |
| de | Seröses Zystadenokarzinom des Pankreas | Pankreatisches seröses Zystadenokarzinom · SCN · Serös-zystische Neoplasien des Pankreas |
| es | Cistoadenocarcinoma seroso de páncreas | Cistoadenocarcinoma pancreático seroso |
| it | Cistoadenocarcinoma sieroso del pancreas | Cistoadenocarcinoma pancreatico sieroso |
| nl | Sereus cystadenocarcinoom van prancreas | Pancreatisch sereus cystadenocarcinoom |
| pt | Cistoadenocarcinoma seroso do pâncreas | |
| pl | Gruczolakotorbielakorak surowiczy trzustki | = en |
| cs | Serózní cystadenokarcinom pankreatu | Pankreatický serózní cystadenokarcinom |
| uk | Серозна цистаденокарцинома підшлункової залози | Серозна цистаденокарцинома підшлункової залози |
| zh | 胰腺浆液性囊腺癌 | 胰腺浆液性囊腺癌 |
| tr | Pankreasın seröz kistadenokarsinomu | Pankreasın seröz kistadenokarsinomu |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | C25.0 | BTNT | attributed | validated |
| ICD-10 | C25.1 | BTNT | attributed | validated |
| ICD-10 | C25.2 | BTNT | attributed | validated |
| ICD-10 | C25.7 | BTNT | attributed | validated |
| ICD-10 | C25.8 | BTNT | attributed | validated |
| ICD-11 | 2C10.0 | NTBT | index | validated |
| MONDO | 0003630 | E | validated | |
| UMLS | C1335315 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:217074Rare carcinoma of pancreas
rare gastroenterological diseases; rare neoplastic diseases
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
4 records| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Annual incidence | <1 / 1 000 000 | 0.002 / 100 000 | Belgium | Value and class | Validated | RARECARE surveillance of rare cancers in Europe[OTHER] |
| Annual incidence | <1 / 1 000 000 | 0.002 / 100 000 | Finland | Value and class | Validated | RARECARE surveillance of rare cancers in Europe[OTHER] |
| Annual incidence | <1 / 1 000 000 | — | Europe | Class only | Validated | RARECARE surveillance of rare cancers in Europe[OTHER] |
| Annual incidence | <1 / 1 000 000 | 0.001 / 100 000 | Germany | Value and class | Validated | RARECARE surveillance of rare cancers in Europe[OTHER] |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/424073
- This record as JSON: /data/d/424073.json