{"orpha":217074,"name":"Rare carcinoma of pancreas","type":"Category","group":"Group of disorders","status":"active","flags":[],"synonyms":["Rare pancreatic carcinoma"],"definition":null,"note":"This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.","url":"https://raremap.alftech.space/d/ORPHA-217074/","orphanet_url":"https://www.orpha.net/en/disease/detail/217074","names":{"fr":{"name":"Carcinome rare du pancréas"},"de":{"name":"Seltenes Pankreaskarzinom","synonyms":["Bauchspeicheldrüsenkrebs, seltener"]},"es":{"name":"Carcinoma raro de páncreas","synonyms":["Carcinoma pancreático raro"]},"it":{"name":"Carcinoma raro del pancreas","synonyms":["Cancro pancreatico","Tumore pancreatico"]},"nl":{"name":"Zeldzaam carcinoom van pancreas","synonyms":["Zeldzaam carcinoom van alvleesklier","Zeldzaam pancreatisch carcinoom"]},"pt":{"name":"Carcinoma pancreático"},"pl":{"name":"Rzadki rak trzustki","synonyms":["Rare pancreatic carcinoma"]},"cs":{"name":"Vzácný karcinom pankreatu","synonyms":["Vzácný pankreatický karcinom"]},"uk":{"name":"Рідкісна карцинома підшлункової залози","synonyms":["Рідкісна карцинома підшлункової залози"]},"zh":{"name":"罕见胰腺癌","synonyms":["罕见胰腺癌"]},"tr":{"name":"Nadir pankreas karsinomu","synonyms":["Nadir pankreas karsinomu"]}},"xrefs":[{"source":"MONDO","code":"16314","qualifier":"E","icd_relation":null,"validated":true},{"source":"MeSH","code":"D010190","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C5680420","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":250908,"name":"Rare neoplastic disease"},"parents":[{"orpha":424033,"name":"Rare epithelial tumor of pancreas","classifications":[152,202]}],"children":[{"orpha":424046,"name":"Acinar cell carcinoma of pancreas","type":"Disease"},{"orpha":1333,"name":"Familial pancreatic carcinoma","type":"Disease"},{"orpha":424058,"name":"Intraductal papillary mucinous carcinoma of pancreas","type":"Disease"},{"orpha":424053,"name":"Mucinous cystadenocarcinoma of the pancreas","type":"Disease"},{"orpha":424065,"name":"Pancreatic solid pseudopapillary neoplasm","type":"Disease"},{"orpha":424073,"name":"Serous cystadenocarcinoma of pancreas","type":"Disease"},{"orpha":424039,"name":"Squamous cell carcinoma of pancreas","type":"Disease"},{"orpha":424080,"name":"Undifferentiated carcinoma with osteoclast-like giant cells of pancreas","type":"Disease"}],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":["Adult"],"prevalence":[{"type":"Annual incidence","qualification":"Value and class","class":"1-5 / 10 000","value":11.79,"area":"Europe","status":"Validated","source":"RARECARE surveillance of rare cancers in Europe 2011[OTHER]"},{"type":"Lifetime Prevalence","qualification":"Value and class","class":"1-9 / 100 000","value":8.3,"area":"Europe","status":"Validated","source":"22033323[PMID]_RARECARE surveillance of rare cancers in Europe[OTHER]"},{"type":"Point prevalence","qualification":"Value and class","class":"1-5 / 10 000","value":15.5,"area":"Europe","status":"Validated","source":"European Medicines Agency 2013[OTHER]_ORPHANET"},{"type":"Annual incidence","qualification":"Value and class","class":"1-9 / 100 000","value":3.9,"area":"Worldwide","status":"Validated","source":"World Health Organization 2008[OTHER]"},{"type":"Point prevalence","qualification":"Value and class","class":"1-9 / 100 000","value":3.5,"area":"Worldwide","status":"Validated","source":"World Health Organization 2008[OTHER]"}],"phenotypes":null}