raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:163531

Chronic cutaneous lupus erythematosus

Type
Clinical group
Group
Group of disorders
Inheritance
Multigenic/multifactorial
Age of onset
Adolescent, Adult, Childhood, Elderly
Status
active

A form of cutaneous lupus erythematosus (CLE) that includes five different forms: discoid lupus erythematosus (DLE), chilblain lupus, hypertrophic or verrucous lupus erythematosus, lupus erythematosus tumidus, and lupus erythematosus panniculitis.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enChronic cutaneous lupus erythematosus
frLupus érythémateux cutané chronique
deLupus erythematodes, kutaner, chronischer
esLupus eritematoso cutáneo crónico
itLupus eritematoso cutaneo cronico
nlChronische cutane lupus erythematosus
ptLupus eritematoso cutâneo crónico
plPrzewlekły toczeń rumieniowy skórny
csChronický kožní lupus
ukХронічний шкірний червоний вовчак
zh慢性皮肤红斑狼疮
trKronik kutanöz lupus eritematozus

Definition in:

2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-11EB51Especificvalidated
MONDO0015574Evalidated
MONDO15574Evalidated
UMLSC0024138Evalidated
MedDRA10057929Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

Children (6):

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card