Hypertrophic or verrucous lupus erythematosus
- Type
- Disease
- Group
- Disorder
- Status
- active
Hypertrophic or verrucous lupus erythematosus is a rare type of chronic cutaneous lupus erythematosus characterized by the appearance of lesions on sun-exposed areas (frequently the extensor surfaces of forearms, face, upper trunk) which vary from squamous violet, painful papules and blackish hyperkeratotic ulcers to depigmented atrophic plaques on the back, hyperkeratotic papules on upper extremities, and disseminated keratoacanthoma-like papulonodular verrucous lesions. Classic discoid lesions and squamous cell carcinoma may be associated. Histopathology reveals follicular plugging, liquefactive basal layer degeneration and a perivascular lymphocytic infiltrate.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Hypertrophic or verrucous lupus erythematosus | |
| fr | Lupus érythémateux verruqueux ou hypertrophique | |
| de | Lupus erythematosus, hypertropher oder verruköser | |
| es | Lupus eritematoso hipertrófico o verrugoso | |
| it | Lupus eritematoso ipertrofico o verrucoso | |
| nl | Hypertrofische of verruceuze lupus erythematosus | |
| pt | Lúpus eritematoso hipertrófico ou verrucoso | |
| pl | Odmiana przerosła ogniskowego tocznia rumieniowatego | |
| cs | Hypertrofický nebo verukózní lupus erythematodes | |
| uk | Гіпертрофічний або верукозний червоний вовчак | |
| zh | 肥厚性或疣状红斑狼疮 | |
| tr | Hipertrofik veya verrüköz lupus eritematozus |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | L93.2 | NTBT | attributed | validated |
| ICD-11 | EB51.Y | NTBT | index | validated |
| MONDO | 0019559 | E | validated | |
| UMLS | C1274838 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:163531Chronic cutaneous lupus erythematosus
rare skin diseases
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
0 recordsNo prevalence record in this release.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/90282
- This record as JSON: /data/d/90282.json