{"orpha":163531,"name":"Chronic cutaneous lupus erythematosus","type":"Clinical group","group":"Group of disorders","status":"active","flags":[],"synonyms":[],"definition":"A form of cutaneous lupus erythematosus (CLE) that includes five different forms: discoid lupus erythematosus (DLE), chilblain lupus, hypertrophic or verrucous lupus erythematosus, lupus erythematosus tumidus, and lupus erythematosus panniculitis.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-163531/","orphanet_url":"https://www.orpha.net/en/disease/detail/163531","names":{"fr":{"name":"Lupus érythémateux cutané chronique","definition":"Forme de lupus érythémateux cutané (LEC) qui comprend cinq formes différentes&nbsp;: lupus érythémateux discoïde (LED), lupus érythémateux type Chilblain, lupus érythémateux hypertrophique ou verruqueux, lupus érythémateux tumidus et panniculite lupique."},"de":{"name":"Lupus erythematodes, kutaner, chronischer"},"es":{"name":"Lupus eritematoso cutáneo crónico","definition":"Es un tipo de lupus eritematoso cutáneo (CLE) que incluye cinco formas diferentes: lupus eritematoso discoide (DLE), lupus perniótico, lupus eritematoso hipertrófico o verrugoso, lupus eritematoso túmido y lupus eritematoso profundo (paniculitis lúpica)."},"it":{"name":"Lupus eritematoso cutaneo cronico","definition":"Il lupus eritematoso cutaneo cronico (CCLE) è una forma di lupus cutaneo eritematoso (CLE; si veda questo termine) che comprende cinque forme: lupus eritematoso discoide (DLE), lupus gelone, lupus eritematoso ipertrofico o verrucoso, lupus timidus eritematoso e lupus eritematoso - panniculite (di vedano questi termini)."},"nl":{"name":"Chronische cutane lupus erythematosus","definition":"Een vorm van cutane lupus erythematosus (CLE) die vijf verschillende vormen omvat: discoïde lupus erythematosus (DLE), chilblain lupus, hypertrofische of verruceuze lupus erythematosus, lupus erythematosus tumidus, en lupus erythematosus panniculitis."},"pt":{"name":"Lupus eritematoso cutâneo crónico"},"pl":{"name":"Przewlekły toczeń rumieniowy skórny"},"cs":{"name":"Chronický kožní lupus"},"uk":{"name":"Хронічний шкірний червоний вовчак","definition":"A form of cutaneous lupus erythematosus (CLE) that includes five different forms: discoid lupus erythematosus (DLE), chilblain lupus, hypertrophic or verrucous lupus erythematosus, lupus erythematosus tumidus, and lupus erythematosus panniculitis."},"zh":{"name":"慢性皮肤红斑狼疮","definition":"皮肤红斑狼疮（CLE）的一种，包括五种不同形式：盘状红斑狼疮（DLE），冻疮样狼疮，肥大性或疣状红斑狼疮，肿胀性红斑狼疮和红斑狼疮性脂膜炎。"},"tr":{"name":"Kronik kutanöz lupus eritematozus"}},"xrefs":[{"source":"ICD-11","code":"EB51","qualifier":"E","icd_relation":"specific","validated":true,"icd11_uri":"1849568465"},{"source":"MONDO","code":"0015574","qualifier":"E","icd_relation":null,"validated":true},{"source":"MONDO","code":"15574","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C0024138","qualifier":"E","icd_relation":null,"validated":true},{"source":"MedDRA","code":"10057929","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":89826,"name":"Rare skin disease"},"parents":[{"orpha":535,"name":"Rare cutaneous lupus erythematosus","classifications":[187]}],"children":[{"orpha":90280,"name":"Chilblain lupus","type":"Disease"},{"orpha":90281,"name":"Discoid lupus erythematosus","type":"Disease"},{"orpha":481662,"name":"Familial Chilblain lupus","type":"Disease"},{"orpha":90282,"name":"Hypertrophic or verrucous lupus erythematosus","type":"Disease"},{"orpha":90285,"name":"Lupus erythematosus panniculitis","type":"Disease"},{"orpha":90283,"name":"Lupus erythematosus tumidus","type":"Disease"}],"genes":[],"genes_via_subtypes":[],"inheritance":["Multigenic/multifactorial"],"onset":["Adolescent","Adult","Childhood","Elderly"],"prevalence":[],"phenotypes":null}