raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:156146

Predominantly small-vessel vasculitis

Type
Clinical group
Group
Group of disorders
Status
active

This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enPredominantly small-vessel vasculitis
frVascularite des vaisseaux de petit calibre
deVaskulitis kleiner Gefäße
esVasculitis de vasos pequeños predominantemente
itVasculite con interessamento prevalente dei piccoli vasi
nlVasculitis van overwegend kleine bloedvaten
ptVasculite predominantemente dos pequenos vasos
plDominujące zapalenie małych naczyń
csVaskulitida převážně malých cév
ukСистемний васкуліт з переважним ураженням судин малого діаметру
zh主要累及小血管的血管炎
trAğırlıklı küçük-damar vasküliti
2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
MONDO15490Evalidated
UMLSC5680653Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

Children (5):

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card