{"orpha":156146,"name":"Predominantly small-vessel vasculitis","type":"Clinical group","group":"Group of disorders","status":"active","flags":[],"synonyms":[],"definition":null,"note":"This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.","url":"https://raremap.alftech.space/d/ORPHA-156146/","orphanet_url":"https://www.orpha.net/en/disease/detail/156146","names":{"fr":{"name":"Vascularite des vaisseaux de petit calibre"},"de":{"name":"Vaskulitis kleiner Gefäße"},"es":{"name":"Vasculitis de vasos pequeños predominantemente"},"it":{"name":"Vasculite con interessamento prevalente dei piccoli vasi"},"nl":{"name":"Vasculitis van overwegend kleine bloedvaten"},"pt":{"name":"Vasculite predominantemente dos pequenos vasos"},"pl":{"name":"Dominujące zapalenie małych naczyń"},"cs":{"name":"Vaskulitida převážně malých cév"},"uk":{"name":"Системний васкуліт з переважним ураженням судин малого діаметру"},"zh":{"name":"主要累及小血管的血管炎"},"tr":{"name":"Ağırlıklı küçük-damar vasküliti"}},"xrefs":[{"source":"MONDO","code":"15490","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C5680653","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":98023,"name":"Rare systemic or rheumatologic disease"},"parents":[{"orpha":52759,"name":"Vasculitis","classifications":[196,198]}],"children":[{"orpha":375,"name":"Anti-glomerular basement membrane disease","type":"Disease"},{"orpha":156152,"name":"Anti-neutrophil cytoplasmic antibody-associated vasculitis","type":"Clinical group"},{"orpha":156149,"name":"Immune complex mediated vasculitis","type":"Category"},{"orpha":140989,"name":"Primary angiitis of the central nervous system","type":"Disease"},{"orpha":425120,"name":"STING-associated vasculopathy with onset in infancy","type":"Disease"}],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":[],"prevalence":[],"phenotypes":null}