raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:156140

Predominantly large-vessel vasculitis

Type
Clinical group
Group
Group of disorders
Status
active

This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enPredominantly large-vessel vasculitis
frVascularite des vaisseaux de gros calibre
deVaskulitis großer Gefäße
esVasculitis con afectación predominante de grandes vasos
itVasculite con interessamento prevalente dei grandi vasi
nlVasculitis van overwegend grote bloedvaten
ptVasculite predominantemente dos grandes vasos
plDominujące zapalenie dużych naczyń
csVaskulitida převážně velkých cév
ukСистемний васкуліт з переважним ураженням судин великого діаметра
zh主要累及大血管的血管炎
trAğırlıklı büyük-damar vasküliti
2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
MONDO15488Evalidated
UMLSC5680657Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

Children (6):

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card