{"orpha":156140,"name":"Predominantly large-vessel vasculitis","type":"Clinical group","group":"Group of disorders","status":"active","flags":[],"synonyms":[],"definition":null,"note":"This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.","url":"https://raremap.alftech.space/d/ORPHA-156140/","orphanet_url":"https://www.orpha.net/en/disease/detail/156140","names":{"fr":{"name":"Vascularite des vaisseaux de gros calibre"},"de":{"name":"Vaskulitis großer Gefäße"},"es":{"name":"Vasculitis con afectación predominante de grandes vasos"},"it":{"name":"Vasculite con interessamento prevalente dei grandi vasi"},"nl":{"name":"Vasculitis van overwegend grote bloedvaten"},"pt":{"name":"Vasculite predominantemente dos grandes vasos"},"pl":{"name":"Dominujące zapalenie dużych naczyń"},"cs":{"name":"Vaskulitida převážně velkých cév"},"uk":{"name":"Системний васкуліт з переважним ураженням судин великого діаметра"},"zh":{"name":"主要累及大血管的血管炎"},"tr":{"name":"Ağırlıklı büyük-damar vasküliti"}},"xrefs":[{"source":"MONDO","code":"15488","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C5680657","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":98023,"name":"Rare systemic or rheumatologic disease"},"parents":[{"orpha":52759,"name":"Vasculitis","classifications":[196,198]}],"children":[{"orpha":117,"name":"Behçet disease","type":"Disease"},{"orpha":1467,"name":"Cogan syndrome","type":"Disease"},{"orpha":397,"name":"Giant cell arteritis","type":"Disease"},{"orpha":228116,"name":"Hughes-Stovin syndrome","type":"Disease"},{"orpha":26137,"name":"Juvenile temporal arteritis","type":"Disease"},{"orpha":3287,"name":"Takayasu arteritis","type":"Disease"}],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":[],"prevalence":[],"phenotypes":null}