raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:100088

Rare thyroid carcinoma

Type
Category
Group
Group of disorders
Age of onset
Adult
Status
active

This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enRare thyroid carcinoma
frCarcinome rare de la thyroïde
deSeltenes Schilddrüsenkarzinom
esCarcinoma de tiroides raro
itCarcinoma tiroideo raro
nlZeldzaam schildkliercarcinoomZeldzaam thyroïdcarcinoom
ptCarcinoma da tiroide raro
plRak tarczycyRzadki rak tarczycy
csKarcinom štítné žlázy
ukРідкісна карцинома щитовидної залози
zh甲状腺癌
trTiroid kanseri
2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
MONDO15075Evalidated
UMLSC5816697Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

Children (6):

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

27 records
TypeClassValueAreaQualificationValidationSource
Annual incidence1-9 / 100 0003.65 / 100 000EuropeValue and classNot yet validated22033323[PMID]_23894154[PMID]
Lifetime Prevalence6-9 / 10 00061.7 / 100 000EuropeValue and classValidated22033323[PMID]_RARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence1-5 / 10 00012.2 / 100 000United StatesValue and classValidatedNational Cancer OTHERitute 2010[OTHER]
Annual incidence1-9 / 100 0003.1 / 100 000WorldwideValue and classValidatedWorld Health Organization 2008[OTHER]
Point prevalence1-5 / 10 00012.7 / 100 000WorldwideValue and classValidatedWorld Health Organization 2008[OTHER]
Annual incidence1-9 / 100 0002.733 / 100 000United KingdomValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence1-5 / 10 00012.86 / 100 000ItalyValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence1-9 / 100 0007.679 / 100 000AustriaValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence1-9 / 100 0003.74 / 100 000BelgiumValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence1-9 / 100 0002.921 / 100 000BulgariaValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence1-9 / 100 0008.329 / 100 000CroatiaValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence1-9 / 100 0006.382 / 100 000Czech RepublicValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence1-9 / 100 0004.803 / 100 000EstoniaValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence1-9 / 100 0006.375 / 100 000FinlandValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence1-9 / 100 0005.526 / 100 000GermanyValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence1-9 / 100 0002.45 / 100 000IrelandValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence1-9 / 100 0004.563 / 100 000LatviaValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence1-9 / 100 0007.905 / 100 000LithuaniaValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence1-9 / 100 0006.344 / 100 000MaltaValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence1-9 / 100 0004.472 / 100 000NorwayValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence1-9 / 100 0004.488 / 100 000PolandValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence1-9 / 100 0008.628 / 100 000PortugalValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence1-9 / 100 0003.991 / 100 000SlovakiaValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence1-9 / 100 0005.649 / 100 000SloveniaValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence1-9 / 100 0005.162 / 100 000SpainValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence1-9 / 100 0006.39 / 100 000SwitzerlandValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence1-9 / 100 0002.373 / 100 000NetherlandsValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]

Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card