raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:99825

Nipah virus disease

Synonyms: Nipah encephalitis · Nipah fever

Type
Disease
Group
Disorder
Age of onset
All ages
Status
active

Nipah virus disease, caused by the Nipah virus, is a recently discovered zoonotic disease characterized by fever, constitutional symptoms and encephalitis, sometimes accompanied by respiratory illness.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enNipah virus diseaseNipah encephalitis · Nipah fever
frMaladie à virus NipahEncéphalite à virus Nipah · Fièvre à virus Nipah
deNipah-ViruskrankheitNipah-Enzephalitis · Nipah-Fieber
esEnfermedad por el virus de NipahEncefalitis de Nipah · Fiebre de Nipah
itMalattia virale di NipahEncefalite di Nipah · Febbre di Nipah
nlNipah-virusziekteEncefalitis door Nipah virus · Koorts door Nipah virus
ptFebre de Nipah
plChoroba wirusowa NipahGorączka Nipah · Zapalenie mózgu Nipah
csOnemocnění způsobené virem NipahNipah encefalitida · Nipah horecka · Nipah horečka
ukВірусна хвороба НіпахЕнцефаліт Ніпа · Лихоманка Ніпа
zh尼帕病毒病尼帕脑炎
trNipah virüsü hastalığıNipah ateşi · Nipah encephalitis

Definition in:

2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-10A85.8NTBTattributedvalidated
ICD-111D63NTBTindexvalidated
MONDO0020499Evalidated
UMLSC1320202Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

2 records
TypeClassValueAreaQualificationValidationSource
Cases/families556 casesWorldwideCase(s)Validated[EXPERT]_World Health Organization[OTHER]
Point prevalence<1 / 1 000 000—WorldwideClass onlyValidatedORPHANET

Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.

6

HPO phenotypes

17 annotations · validated 2016-06-01
HPOTerm (as annotated by Orphanet)Diagnostic
Very frequent (99-80%)
HP:0002039Anorexia
HP:0012378Fatigue
HP:0001945Fever
HP:0002315Headache
HP:0003326Myalgia
HP:0002017Nausea and vomiting
HP:0100776Recurrent pharyngitis
Frequent (79-30%)
HP:0002383Infectious encephalitis
HP:0001336Myoclonus
HP:0001250Seizure
HP:0001337Tremor
HP:0002321Vertigo
Occasional (29-5%)
HP:0001259Coma
HP:0012735Cough
HP:0002615Hypotension
HP:0000751Personality changes
HP:0002098Respiratory distress

Run the differential on the 7 obligate / very frequent terms

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Sources for this card