{"orpha":99825,"name":"Nipah virus disease","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":["Nipah encephalitis","Nipah fever"],"definition":"Nipah virus disease, caused by the Nipah virus, is a recently discovered zoonotic disease characterized by fever, constitutional symptoms and encephalitis, sometimes accompanied by respiratory illness.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-99825/","orphanet_url":"https://www.orpha.net/en/disease/detail/99825","names":{"fr":{"name":"Maladie à virus Nipah","synonyms":["Encéphalite à virus Nipah","Fièvre à virus Nipah"],"definition":"La maladie à virus Nipah est une maladie zoonotique récemment découverte, causée par le virus Nipah et caractérisée par une fièvre, des symptômes constitutionnels et une encéphalite parfois accompagnée de manifestations respiratoires."},"de":{"name":"Nipah-Viruskrankheit","synonyms":["Nipah-Enzephalitis","Nipah-Fieber"],"definition":"Die Nipah-Virus-Krankheit, eine vor kurzem entdeckte Zoonose, wird durch das Nipah-Virus verursacht. Typisch sind Fieber, Allgemeinsymptome und Enzephalitis, manchmal begleitet von einer Atemwegserkrankung."},"es":{"name":"Enfermedad por el virus de Nipah","synonyms":["Encefalitis de Nipah","Fiebre de Nipah"],"definition":"La enfermedad por el virus Nipah, causada por el virus Nipah, es una enfermedad zoonótica recientemente descubierta que se caracteriza por fiebre, síntomas constitucionales y encefalitis, a veces acompañada por enfermedad respiratoria."},"it":{"name":"Malattia virale di Nipah","synonyms":["Encefalite di Nipah","Febbre di Nipah"],"definition":"La malattia da virus Nipah, causata dal virus Nipah, è una malattia zoonotica, descritta di recente, caratterizzata da febbre ed encefalite, associate occasionalmente a una malattia respiratoria."},"nl":{"name":"Nipah-virusziekte","synonyms":["Encefalitis door Nipah virus","Koorts door Nipah virus"],"definition":"Nipah-virusziekte, veroorzaakt door het Nipahvirus, is een recent ontdekte zoönotische ziekte die gekenmerkt wordt door koorts, constitutionele symptomen en encefalitis, soms vergezeld van een ademhalingsziekte."},"pt":{"name":"Febre de Nipah"},"pl":{"name":"Choroba wirusowa Nipah","synonyms":["Gorączka Nipah","Zapalenie mózgu Nipah"]},"cs":{"name":"Onemocnění způsobené virem Nipah","synonyms":["Nipah encefalitida","Nipah horecka","Nipah horečka"]},"uk":{"name":"Вірусна хвороба Ніпах","synonyms":["Енцефаліт Ніпа","Лихоманка Ніпа"],"definition":"Nipah virus disease, caused by the Nipah virus, is a recently discovered zoonotic disease characterized by fever, constitutional symptoms and encephalitis, sometimes accompanied by respiratory illness."},"zh":{"name":"尼帕病毒病","synonyms":["尼帕脑炎"],"definition":"尼帕病毒病是由尼帕病毒引起的一种新发现的人畜共患病，以发热、全身性症状和脑炎为特征，有时还伴有呼吸道疾病。"},"tr":{"name":"Nipah virüsü hastalığı","synonyms":["Nipah ateşi","Nipah encephalitis"]}},"xrefs":[{"source":"ICD-10","code":"A85.8","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"1D63","qualifier":"NTBT","icd_relation":"index","validated":true,"icd11_uri":"661628832"},{"source":"MONDO","code":"0020499","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C1320202","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":68416,"name":"Rare infectious disease"},"parents":[{"orpha":98252,"name":"Infectious encephalitis","classifications":[181,203]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":["All ages"],"prevalence":[{"type":"Cases/families","qualification":"Case(s)","class":null,"value":556.0,"area":"Worldwide","status":"Validated","source":"[EXPERT]_World Health Organization[OTHER]"},{"type":"Point prevalence","qualification":"Class only","class":"<1 / 1 000 000","value":0.0,"area":"Worldwide","status":"Validated","source":"ORPHANET"}],"phenotypes":{"validation_status":"y","online":"y","validation_date":"2016-06-01","source":null,"terms":[{"hpo":"HP:0002039","label":"Anorexia","frequency":"Very frequent (99-80%)","criteria":null},{"hpo":"HP:0012378","label":"Fatigue","frequency":"Very frequent (99-80%)","criteria":null},{"hpo":"HP:0001945","label":"Fever","frequency":"Very frequent (99-80%)","criteria":null},{"hpo":"HP:0002315","label":"Headache","frequency":"Very frequent (99-80%)","criteria":null},{"hpo":"HP:0003326","label":"Myalgia","frequency":"Very frequent (99-80%)","criteria":null},{"hpo":"HP:0002017","label":"Nausea and vomiting","frequency":"Very frequent (99-80%)","criteria":null},{"hpo":"HP:0100776","label":"Recurrent pharyngitis","frequency":"Very frequent (99-80%)","criteria":null},{"hpo":"HP:0002383","label":"Infectious encephalitis","frequency":"Frequent (79-30%)","criteria":null},{"hpo":"HP:0001336","label":"Myoclonus","frequency":"Frequent (79-30%)","criteria":null},{"hpo":"HP:0001250","label":"Seizure","frequency":"Frequent (79-30%)","criteria":null},{"hpo":"HP:0001337","label":"Tremor","frequency":"Frequent (79-30%)","criteria":null},{"hpo":"HP:0002321","label":"Vertigo","frequency":"Frequent (79-30%)","criteria":null},{"hpo":"HP:0001259","label":"Coma","frequency":"Occasional (29-5%)","criteria":null},{"hpo":"HP:0012735","label":"Cough","frequency":"Occasional (29-5%)","criteria":null},{"hpo":"HP:0002615","label":"Hypotension","frequency":"Occasional (29-5%)","criteria":null},{"hpo":"HP:0000751","label":"Personality changes","frequency":"Occasional (29-5%)","criteria":null},{"hpo":"HP:0002098","label":"Respiratory distress","frequency":"Occasional (29-5%)","criteria":null}]}}