Pleuro-pericardial cyst
- Type
- Morphological anomaly
- Group
- Disorder
- Inheritance
- Not applicable
- Status
- active
Pleuro-pericardial cyst is a rare, mostly congenital, pericardium anomaly characterized by the presence of, usually asymptomatic, cysts which are typically located in the right costophrenic angle and are usually incidentally diagnosed. On occasion, it manifests with chest pain, dyspnea, tachycardia, persistent cough or cardiac arrhythmias. The condition is usually benign, but rare complications, such as cardiac tamponade, cardiogenic shock, mitral valve prolapse, hoarseness atrial fibrillation, right ventricular outflow, tract obstruction, spontaneous internal hemorrhage, pulmonary stenosis and sudden death, may occur.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Pleuro-pericardial cyst | |
| fr | Kystes pleuro-péricardiques | |
| de | Zyste, pleuroperikardiale | Pleuroperikardzyste |
| es | Quiste pleuropericárdico | |
| it | Cisti pleuro-pericardica | |
| nl | Pleuropericardiale cyste | |
| pt | Quisto pleuro-pericárdico | |
| pl | Torbiel opłucnowo-osierdziowa | |
| cs | Pleuroperikardiální cysta | |
| uk | Плевро-перикардіальна кіста | |
| zh | 胸膜心包囊肿 | |
| tr | Plevra-perikardiyal kist |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | Q24.8 | NTBT | attributed | validated |
| ICD-11 | LA8D | NTBT | index | validated |
| MONDO | 0020456 | E | validated | |
| UMLS | C0345141 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:2846Congenital pericardium anomaly
rare developmental anomalies during embryogenesis; rare cardiac malformations
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
0 recordsNo prevalence record in this release.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/99131
- This record as JSON: /data/d/99131.json