ORPHA:98843

Classic Hodgkin lymphoma, nodular sclerosis type

This disease is described under Classic Hodgkin lymphoma

Names in Orphadata languages

12 of 12 languages

Lang	Name	Synonyms
en	Classic Hodgkin lymphoma, nodular sclerosis type
fr	Lymphome de Hodgkin classique type sclérosant nodulaire
de	Klassisches Hodgkin-Lymphom, nodulär-sklerosierendes
es	Linfoma de Hodgkin clásico con esclerosis nodular
it	Linfoma di Hodgkin classico, tipo nodulare sclerosante
nl	Klassiek Hodgkin-lymfoom, type nodulaire sclerose
pt	Linfoma de Hodgkin clássico, esclerose nodular
pl	Klasyczny chłoniak Hodgkina, typ ze stwardnieniem guzkowym
cs	Klasický Hodgkinův lymfom, typ nodulární sklerózy
uk	Класична лімфома Ходжкіна, тип вузликового склерозу
zh	经典霍奇金淋巴瘤结节硬化型
tr	Klasik Hodgkin lenfoma, nodüler skleroz tipi

qualifier = Orphanet mapping relation

Source	Code	Qualifier	ICD relation	Validation
ICD-10	C81.1	E	specific	validated
ICD-11	2B30.10	E	specific	validated
MONDO	0020327	E		validated
MONDO	4665	E		validated
UMLS	C0152268	E		validated
MedDRA	10020244	E		validated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

ORPHA:391Classic Hodgkin lymphoma
rare hematological diseases; rare neoplastic diseases; rare transplant-related disorders

No children.

1 direct

Gene	Association	Status	HGNC	Ensembl	OMIM	Locus	Name	Source of validation
KLHDC8B	Candidate gene tested in	Not yet assessed	HGNC:28557	ENSG00000185909	613169	3p21.31	kelch domain containing 8B	19706467[PMID]

1 record

Type	Class	Value	Area	Qualification	Validation	Source
Annual incidence	1-9 / 100 000	1.28 / 100 000	Europe	Value and class	Validated	RARECARE surveillance of rare cancers in Europe[OTHER]

Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.

Orphanet has no HPO annotation for this code in this release.