raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:98291

Lymphoproliferative disease associated with primary immune disease

Type
Category
Group
Group of disorders
Age of onset
Childhood
Status
active

This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enLymphoproliferative disease associated with primary immune disease
frSyndrome lymphoprolifératif associé à un déficit immunitaire primaire
deLymphoproliferative Krankheit mit assoziiertem primären Imundefekt
esEnfermedad linfoproliferativa asociada con la inmunodeficiencia primaria
itMalattia linfoproliferativa associata a malattia immune primaria
nlLymfoproliferatieve ziekte geassocieerd met primaire immuunziekte
ptDoença linfoproliferativa associada a doença imune primária
plChoroba limfoproliferacyjna z towarzyszącym pierwotnym niedoborem odporności
csLymfoproliferativní onemocnění spojená s primární poruchou imunity
ukЛімфопроліферативне захворювання, повязане з первинним імунним захворюванням
zh原发性免疫疾病相关淋巴增殖性疾病
trPrimer bağışıklık hastalığı -ilişkili lenfoproliferatif hastalık
2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
UMLSC5681532Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card