{"orpha":98291,"name":"Lymphoproliferative disease associated with primary immune disease","type":"Category","group":"Group of disorders","status":"active","flags":[],"synonyms":[],"definition":null,"note":"This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.","url":"https://raremap.alftech.space/d/ORPHA-98291/","orphanet_url":"https://www.orpha.net/en/disease/detail/98291","names":{"fr":{"name":"Syndrome lymphoprolifératif associé à un déficit immunitaire primaire"},"de":{"name":"Lymphoproliferative Krankheit mit assoziiertem primären Imundefekt"},"es":{"name":"Enfermedad linfoproliferativa asociada con la inmunodeficiencia primaria"},"it":{"name":"Malattia linfoproliferativa associata a malattia immune primaria"},"nl":{"name":"Lymfoproliferatieve ziekte geassocieerd met primaire immuunziekte"},"pt":{"name":"Doença linfoproliferativa associada a doença imune primária"},"pl":{"name":"Choroba limfoproliferacyjna z towarzyszącym pierwotnym niedoborem odporności"},"cs":{"name":"Lymfoproliferativní onemocnění spojená s primární poruchou imunity"},"uk":{"name":"Лімфопроліферативне захворювання, повязане з первинним імунним захворюванням"},"zh":{"name":"原发性免疫疾病相关淋巴增殖性疾病"},"tr":{"name":"Primer bağışıklık hastalığı -ilişkili lenfoproliferatif hastalık"}},"xrefs":[{"source":"UMLS","code":"C5681532","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":250908,"name":"Rare neoplastic disease"},"parents":[{"orpha":98290,"name":"Immunodeficiency-associated lymphoproliferative disease","classifications":[194,202,233]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":["Childhood"],"prevalence":[],"phenotypes":null}