Twin to twin transfusion syndrome
Synonyms: Feto-fetal transfusion syndrome
- Type
- Disease
- Group
- Disorder
- Status
- active
Twin twin transfusion syndrome (TTTS) is a rare condition seen in twin monochorionic pregnancies, typically developing during the 15-26 week gestation period and usually due to unbalanced intertwin placental anastomoses, where an unequal exchange of blood between twins causes oligohydramnios in one sac and polyhydramnios in the other which can lead to a high perinatal mortality rate and a high rate of disability in survivors if left untreated
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Twin to twin transfusion syndrome | Feto-fetal transfusion syndrome |
| fr | Syndrome de transfusion foeto-foetale | STT · Syndrome transfuseur-transfusé |
| de | Zwillings-Transfusions-Syndrom | FFTS · Fetofetales Transfusions-Syndrom · TTTS |
| es | Síndrome de transfusión gemelo-gemelo | Síndrome de transfusión feto-fetal |
| it | Sindrome da trasfusione gemello-gemello | Sindrome della trasfusione feto-fetale |
| nl | Tweelingtransfusiesyndroom | Foeto-foetaal transfusiesyndroom |
| pt | Síndrome de transfusão de gémeo-para-gémeo | |
| pl | Zespół transfuzji międzypłodowej | Zespół przetoczenia krwi między płodami |
| cs | Syndrom feto-fetální transfuze | Feto-fetální transfuzní syndrom |
| uk | Синдром трансфузії від близнюка до близнюка | Фето-фетальний трансфузійний синдром |
| zh | 双胎输血综合征 | 双胎输血综合征 |
| tr | İkizden ikize transfüzyon sendromu | Feto-fetal transfüzyon sendromu |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | O43.0 | NTBT | inclusion | validated |
| ICD-10 | P02.3 | NTBT | index | validated |
| ICD-11 | JA8A.0 | NTBT | index | validated |
| MONDO | 0019805 | E | validated | |
| MeSH | D005330 | E | validated | |
| UMLS | C2909036 | E | validated | |
| GARD | 325 | E | validated | |
| MedDRA | 10058328 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:617310Rare disorder due to unbalanced inter-twin blood transfusion
rare gynecological and obstetric diseases
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
0 recordsNo prevalence record in this release.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/95431
- This record as JSON: /data/d/95431.json