raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:93214

OBSOLETE: Familial idiopathic steroid-resistant nephrotic syndrome with diffuse mesangial proliferation

inactive · referred to ORPHA:656Hereditary steroid-resistant nephrotic syndrome

Type
Histopathological subtype
Group
Subtype of disorder
Status
inactive
Flag
Obsolete entity

This entity has been obsoleted from the Orphanet nomenclature of rare diseases.<br/><br/>Instead, consider using Genetic steroid-resistant nephrotic syndrome

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enOBSOLETE: Familial idiopathic steroid-resistant nephrotic syndrome with diffuse mesangial proliferation
frOBSOLETE : Syndrome néphrotique idiopathique familial corticorésistant avec prolifération mésangiale diffuse
deOBSOLET: Nephrotisches Syndrom, familiäres idiopathisches steroid-resistentes, mit diffuser mesangialer Proliferation
esOBSOLETO: Síndrome nefrótico familiar idiopático resistente a esteroides con proliferación mesangial difusa
itOBSOLETO: Sindrome nefrosica idiopatica steroido-resistente con proliferazione mesangiale diffusa, forma familiare
nlOBSOLEET: Familiaal idiopathisch steroïderesistent nefrotisch syndroom met diffuse mesangiale proliferatie
ptOBSOLETO: Síndrome nefrótica corticorresistente idiopática familiar com proliferação mesangial difusa
plNIEAKTUALNE: Rodzinny steroidooporny idiopatyczny zespól nerczycowy z rozlana proliferacja mezangium
csNEAKTUÁLNÍ: Familiární idiopatický nefrotický syndrom rezistentní na steroidy s difuzní proliferací mesangia
ukЗАСТАРІЛО: Сімейний ідіопатичний стероїдорезистентний нефротичний синдром з дифузною мезангіальною проліферацією
zh弃用:家族性激素敏感型原发性肾病综合征伴弥漫性系膜增生
trEski adı: Yaygın mezangial proliferasyon ile seyreden ailesel idiyopatik steroide dirençli nefrotik sendrom
2

Cross-references

qualifier = Orphanet mapping relation

No cross-references in this release.

3

Classification

Not placed in any Orphanet classification in this release.

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card