{"orpha":93214,"name":"OBSOLETE: Familial idiopathic steroid-resistant nephrotic syndrome with diffuse mesangial proliferation","type":"Histopathological subtype","group":"Subtype of disorder","status":"inactive","flags":["Obsolete entity"],"synonyms":[],"definition":null,"note":"This entity has been obsoleted from the Orphanet nomenclature of rare diseases.<br/><br/>Instead, consider using Genetic steroid-resistant nephrotic syndrome","url":"https://raremap.alftech.space/d/ORPHA-93214/","orphanet_url":"https://www.orpha.net/en/disease/detail/93214","names":{"fr":{"name":"OBSOLETE : Syndrome néphrotique idiopathique familial corticorésistant avec prolifération mésangiale diffuse"},"de":{"name":"OBSOLET: Nephrotisches Syndrom, familiäres idiopathisches steroid-resistentes, mit diffuser mesangialer Proliferation"},"es":{"name":"OBSOLETO: Síndrome nefrótico familiar idiopático resistente a esteroides con proliferación mesangial difusa"},"it":{"name":"OBSOLETO: Sindrome nefrosica idiopatica steroido-resistente con proliferazione mesangiale diffusa, forma familiare"},"nl":{"name":"OBSOLEET: Familiaal idiopathisch steroïderesistent nefrotisch syndroom met diffuse mesangiale proliferatie"},"pt":{"name":"OBSOLETO: Síndrome nefrótica corticorresistente idiopática familiar com proliferação mesangial difusa"},"pl":{"name":"NIEAKTUALNE: Rodzinny steroidooporny idiopatyczny zespól nerczycowy z rozlana proliferacja mezangium"},"cs":{"name":"NEAKTUÁLNÍ: Familiární idiopatický nefrotický syndrom rezistentní na steroidy s difuzní proliferací mesangia"},"uk":{"name":"ЗАСТАРІЛО: Сімейний ідіопатичний стероїдорезистентний нефротичний синдром з дифузною мезангіальною проліферацією"},"zh":{"name":"弃用：家族性激素敏感型原发性肾病综合征伴弥漫性系膜增生"},"tr":{"name":"Eski adı: Yaygın mezangial proliferasyon ile seyreden ailesel idiyopatik steroide dirençli nefrotik sendrom"}},"xrefs":[],"associations":[{"type":"Referred to","orpha":656,"name":"Hereditary steroid-resistant nephrotic syndrome"}],"incoming_associations":[],"preferential_parent":null,"parents":[],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":[],"prevalence":[],"phenotypes":null}