raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:90398

Localized lichen myxedematosus with mixed features of different subtypes

Type
Clinical subtype
Group
Subtype of disorder
Age of onset
Adult, Elderly
Status
active

Localized lichen myxedematosus (LM) with mixed features of different subtypes is a form of atypical lichen myxedematosus, characterized by mixed features of the 5 subtypes of localized LM which are: discrete papular LM, acral persistent papular mucinosis, self-healing papular mucinosis, papular mucinosis of infancy, and nodular LM.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enLocalized lichen myxedematosus with mixed features of different subtypes
frLichen myxoedémateux localisé à présentation mixte
deLichen myxoedematosus, lokalisierter, mit gemischten Eigenschaften der Subtypen
esLiquen mixedematoso localizado con rasgos mixtos de subtipos diferentes
itLichen mixedematoso localizzato associato a diversi sottotipi
nlGelokaliseerde lichen myxoedematosus met gemengde eigenschappen van verschillende subtypes
ptLíquen mixedematoso localizado com características de diferentes subtipos
plZlokalizowany liszaj śluzowaty z objawami mieszanymi w różnych podtypach
csLokalizovaný lichen myxedematosus se smíšenými prvky z jiných podtypů
ukЛокалізований мікседематозний ліхен зі змішаними ознаками різних підтипів
zh混合亚型局限性粘液水肿性苔癣
trFarklı alt tiplerin karma özellikleri ile seyreden lokalize liken miksödematozus

Definition in:

2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-10L98.5NTBTattributedvalidated
ICD-11EB90.11NTBTattributedvalidated
MONDO0019583Evalidated
UMLSC5681465Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

2 records
TypeClassValueAreaQualificationValidationSource
Cases/families10 casesWorldwideCase(s)ValidatedORPHANET
Point prevalence<1 / 1 000 000—WorldwideClass onlyValidatedORPHANET

Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card