{"orpha":90398,"name":"Localized lichen myxedematosus with mixed features of different subtypes","type":"Clinical subtype","group":"Subtype of disorder","status":"active","flags":[],"synonyms":[],"definition":"Localized lichen myxedematosus (LM) with mixed features of different subtypes is a form of atypical lichen myxedematosus, characterized by mixed features of the 5 subtypes of localized LM which are: discrete papular LM, acral persistent papular mucinosis, self-healing papular mucinosis, papular mucinosis of infancy, and nodular LM.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-90398/","orphanet_url":"https://www.orpha.net/en/disease/detail/90398","names":{"fr":{"name":"Lichen myxoedémateux localisé à présentation mixte","definition":"Le lichen myxoedémateux (LM) localisé à présentation mixte est une forme de lichen myxoedémateux atypique caractérisée par un mélange des symptômes des 5 sous-types du LM localisé, à savoir : le LM discret, la mucinose papuleuse acrale persistante, la mucinose cutanée juvénile spontanément régressive, la mucinose cutanée infantile, et le LM nodulaire."},"de":{"name":"Lichen myxoedematosus, lokalisierter, mit gemischten Eigenschaften der Subtypen"},"es":{"name":"Liquen mixedematoso localizado con rasgos mixtos de subtipos diferentes","definition":"El liquen mixedematoso (LM) localizado con características mixtas de diferentes subtipos es una forma de liquen mixedematoso atípico, caracterizado por rasgos mixtos de los 5 subtipos de LM localizado, que son: LM papular discreto, mucinosis papular acral persistente , mucinosis papular autocurativa, mucinosis papular de la infancia y LM nodular."},"it":{"name":"Lichen mixedematoso localizzato associato a diversi sottotipi"},"nl":{"name":"Gelokaliseerde lichen myxoedematosus met gemengde eigenschappen van verschillende subtypes","definition":"Gelokaliseerde lichen myxoedematosus (LM) met gemengde eigenschappen van verschillende subtypes is een vorm van atypische lichen myxoedematosus (zie deze term) die wordt gekarakteriseerd door een vermenging van de kenmerken van deze 5 subtypes van gelokaliseerde LM: discrete papulaire LM, acrale persistente papulaire mucinose, zelfhelende papulaire mucinose, papulaire mucinose in de zuigelingentijd, en nodulaire LM (zie deze termen)."},"pt":{"name":"Líquen mixedematoso localizado com características de diferentes subtipos"},"pl":{"name":"Zlokalizowany liszaj śluzowaty z objawami mieszanymi w różnych podtypach"},"cs":{"name":"Lokalizovaný lichen myxedematosus se smíšenými prvky z jiných podtypů"},"uk":{"name":"Локалізований мікседематозний ліхен зі змішаними ознаками різних підтипів","definition":"Localized lichen myxedematosus (LM) with mixed features of different subtypes is a form of atypical lichen myxedematosus (see this term), characterized by mixed features of the 5 subtypes of localized LM which are: discrete papular LM, acral persistent papular mucinosis, self-healing papular mucinosis, papular mucinosis of infancy, and nodular LM (see these terms)."},"zh":{"name":"混合亚型局限性粘液水肿性苔癣"},"tr":{"name":"Farklı alt tiplerin karma özellikleri ile seyreden lokalize liken miksödematozus"}},"xrefs":[{"source":"ICD-10","code":"L98.5","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"EB90.11","qualifier":"NTBT","icd_relation":"attributed","validated":true,"icd11_uri":"null"},{"source":"MONDO","code":"0019583","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C5681465","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":89826,"name":"Rare skin disease"},"parents":[{"orpha":86797,"name":"Atypical lichen myxedematosus","classifications":[187]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":["Adult","Elderly"],"prevalence":[{"type":"Cases/families","qualification":"Case(s)","class":null,"value":10.0,"area":"Worldwide","status":"Validated","source":"ORPHANET"},{"type":"Point prevalence","qualification":"Class only","class":"<1 / 1 000 000","value":0.0,"area":"Worldwide","status":"Validated","source":"ORPHANET"}],"phenotypes":null}