ORPHA:90393
Nodular lichen myxedematosus
Synonyms: Atypical tuberous myxedema of Jadassohn-Dosseker
- Type
- Disease
- Group
- Disorder
- Status
- active
Nodular lichen myxedematosus is a rare form of localized lichen myxedematosus characterized by the development of skin-coloured mucinous nodules on the limbs and trunk, with mild or absent papular eruption.
1
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Nodular lichen myxedematosus | Atypical tuberous myxedema of Jadassohn-Dosseker |
| fr | Lichen myxoedémateux nodulaire | Myoxoedème tubéreux atypique de Jadassohn-Dosseker |
| de | Lichen myxoedematosus, nodulärer | Myxödem, atypisches tuberöses, Typ Jadassohn-Dosseker |
| es | Liquen mixedematoso nodular | Mixedema de Jadassohn-Dosseker tuberoso atípico |
| it | Lichen mixedematoso nodulare | Mixedema tuberoso atipico di Jadassohn-Dosseker |
| nl | Nodulaire lichen myxoedematosus | Atypisch tubereus myxoedeem van Jadassohn-Dosseker |
| pt | Líquen mixedematoso nodular | |
| pl | Liszaj śluzowaty odmiana guzkowa | Atypowy liszaj śluzowaty typu Jadassohna i Dossekera |
| cs | Nodulární myxedematózní lichen | Atypický tuberózní myxedém Jadassohnův-Dossekerův · Atypický tuberózní myxedém Jadassohn-Dossekerův |
| uk | Вузлуватий лишай мікседематозний | Атипова туберозна мікседема Жадассона-Доссекера |
| zh | 结节性粘液水肿性苔癣 | 非典型 Jadassohn-Dosseker结节粘液性水肿 |
| tr | Nodüler liken miksödemöz | Jadassohn-Dosseker'in atipik yumrulu miksödemi |
Definition in:
2
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | L98.5 | NTBT | attributed | validated |
| ICD-11 | EB90.11 | NTBT | attributed | validated |
| MONDO | 0019578 | E | validated | |
| UMLS | C4273968 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
3
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:86795Localized lichen myxedematosus
rare skin diseases
No children.
4
Genes
0 directOrphanet records no gene directly on this code.
5
Prevalence and incidence
0 recordsNo prevalence record in this release.
6
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
7
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/90393
- This record as JSON: /data/d/90393.json