Localized lichen myxedematosus
Synonyms: Papular mucinosis
- Type
- Clinical group
- Group
- Group of disorders
- Status
- active
A group of skin diseases characterized by the development of papules, nodules and/or plaques with mucin deposits and a variable degree of fibrosis in the absence of thyroid disease. The group comprises five sub-forms: nodular lichen myxedematosus, discrete papular lichen myxedematosus, papular mucinosis of infancy, acral persistent papular mucinosis and self-healing papular mucinosis.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Localized lichen myxedematosus | Papular mucinosis |
| fr | Lichen myxoedémateux localisé | Mucinose papuleuse |
| de | Lichen myxoedematosus, lokalisierter | Muzinose, papulöse |
| es | Liquen mixedematoso localizado | Mucinosis papular |
| it | Lichen mixedematoso localizzato | Mucinosi papulosa |
| nl | Gelokaliseerde lichen myxoedematosus | Papulaire mucinose |
| pt | Líquen mixedematoso localizado | |
| pl | Liszaj śluzowaty ograniczony | Liszaj śluzowaty |
| cs | Lokalizovaný lichen myxedematosus | Papulární mucinóza |
| uk | Локалізований мікседематозний ліхен | Папульозний муциноз |
| zh | 局限性粘液水肿性苔癣 | 丘疹性黏蛋白病 |
| tr | Lokalize liken miksödemöz | Papüler müsinoz |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-11 | EB90.11 | E | specific | validated |
| MONDO | 0019446 | E | validated | |
| UMLS | C5575846 | E | validated | |
| GARD | 7321 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:402007Lichen myxedematosus
rare skin diseases
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
0 recordsNo prevalence record in this release.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/86795
- This record as JSON: /data/d/86795.json