ORPHA:875
Primary pediatric heart tumor
Synonyms: Cardiac tumor of child · Heart tumor of child
- Type
- Disease
- Group
- Disorder
- Inheritance
- Not applicable
- Age of onset
- Childhood
- Status
- active
Cardiac tumours are benign or malignant neoplasms arising primarily in the inner lining, muscle layer, or the surrounding pericardium of the heart. They can be primary or metastatic.
1
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Primary pediatric heart tumor | Cardiac tumor of child · Heart tumor of child |
| fr | Tumeur cardiaque primaire de l'enfant | |
| de | Herztumor, primärer, des Kindes | Primärer kardialer Tumor des Kindes |
| es | Tumor cardíaco primario pediátrico | Tumor cardíaco del niño · Tumor de corazón del niño |
| it | Tumore cardiaco del bambino | Tumore cardiaco pediatrico primitivo |
| nl | Primaire pediatrische harttumor | Cardiale tumor bij kinderen · Harttumor bij kinderen · Primaire pediatrische cardiale tumor |
| pt | Tumor cardíaco primário pediátrico | |
| pl | Pierwotny dziecięcy guz serca | Dziecięcy guz serca · Cardiac tumor of child |
| cs | Srdeční nádor u dětí | Kardiální nádor u dětí · Primární nádor srdce u dětí |
| uk | Первинна дитяча пухлина серця | Пухлина серця у дитини · Пухлина серця у дитини |
| zh | 原发性小儿心脏肿瘤 | 儿童心脏肿瘤 |
| tr | Primer pediatrik kalp tümörü | Çocuklarda kalp tümörü · Çocuklarda kardiyak tümör |
Definition in:
2
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | C38.0 | NTBT | attributed | validated |
| ICD-10 | D15.1 | NTBT | attributed | validated |
| ICD-11 | 2F01 | NTBT | index | validated |
| MONDO | 0019494 | E | validated | |
| UMLS | C4274356 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
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Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:168194Rare cardiac tumor
rare cardiac diseases; rare neoplastic diseases
No children.
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Genes
0 directOrphanet records no gene directly on this code.
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Prevalence and incidence
1 record| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Point prevalence | Unknown | — | Worldwide | Class only | Not yet validated | ORPHANET |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
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HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
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Sources for this card
- Orphanet page: orpha.net/en/disease/detail/875
- This record as JSON: /data/d/875.json