raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:875

Primary pediatric heart tumor

Synonyms: Cardiac tumor of child · Heart tumor of child

Type
Disease
Group
Disorder
Inheritance
Not applicable
Age of onset
Childhood
Status
active

Cardiac tumours are benign or malignant neoplasms arising primarily in the inner lining, muscle layer, or the surrounding pericardium of the heart. They can be primary or metastatic.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enPrimary pediatric heart tumorCardiac tumor of child · Heart tumor of child
frTumeur cardiaque primaire de l'enfant
deHerztumor, primärer, des KindesPrimärer kardialer Tumor des Kindes
esTumor cardíaco primario pediátricoTumor cardíaco del niño · Tumor de corazón del niño
itTumore cardiaco del bambinoTumore cardiaco pediatrico primitivo
nlPrimaire pediatrische harttumorCardiale tumor bij kinderen · Harttumor bij kinderen · Primaire pediatrische cardiale tumor
ptTumor cardíaco primário pediátrico
plPierwotny dziecięcy guz sercaDziecięcy guz serca · Cardiac tumor of child
csSrdeční nádor u dětíKardiální nádor u dětí · Primární nádor srdce u dětí
ukПервинна дитяча пухлина серцяПухлина серця у дитини · Пухлина серця у дитини
zh原发性小儿心脏肿瘤儿童心脏肿瘤
trPrimer pediatrik kalp tümörüÇocuklarda kalp tümörü · Çocuklarda kardiyak tümör

Definition in:

2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-10C38.0NTBTattributedvalidated
ICD-10D15.1NTBTattributedvalidated
ICD-112F01NTBTindexvalidated
MONDO0019494Evalidated
UMLSC4274356Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

1 record
TypeClassValueAreaQualificationValidationSource
Point prevalenceUnknown—WorldwideClass onlyNot yet validatedORPHANET

Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card