{"orpha":875,"name":"Primary pediatric heart tumor","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":["Cardiac tumor of child","Heart tumor of child"],"definition":"Cardiac tumours are benign or malignant neoplasms arising primarily in the inner lining, muscle layer, or the surrounding pericardium of the heart. They can be primary or metastatic.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-875/","orphanet_url":"https://www.orpha.net/en/disease/detail/875","names":{"fr":{"name":"Tumeur cardiaque primaire de l'enfant","definition":"Les tumeurs cardiaques sont des tumeurs malignes ou bénignes survenant principalement dans l'endocarde, le myocarde, ou le péricarde. Elles peuvent être primaires ou métastatiques."},"de":{"name":"Herztumor, primärer, des Kindes","synonyms":["Primärer kardialer Tumor des Kindes"]},"es":{"name":"Tumor cardíaco primario pediátrico","synonyms":["Tumor cardíaco del niño","Tumor de corazón del niño"],"definition":"Los tumores cardíacos son neoplasias benignas o malignas que se originan principalmente en el revestimiento interno, la capa muscular o el pericardio circundante del corazón. Pueden ser primarios o metastásicos."},"it":{"name":"Tumore cardiaco del bambino","synonyms":["Tumore cardiaco pediatrico primitivo"]},"nl":{"name":"Primaire pediatrische harttumor","synonyms":["Cardiale tumor bij kinderen","Harttumor bij kinderen","Primaire pediatrische cardiale tumor"],"definition":"Harttumoren zijn goed- of kwaadaardige neoplasmata, die hoofdzakelijk ontstaan in endocard, myocard of pericard. Ze kunnen primair of metastatisch zijn."},"pt":{"name":"Tumor cardíaco primário pediátrico"},"pl":{"name":"Pierwotny dziecięcy guz serca","synonyms":["Dziecięcy guz serca","Cardiac tumor of child"]},"cs":{"name":"Srdeční nádor u dětí","synonyms":["Kardiální nádor u dětí","Primární nádor srdce u dětí"]},"uk":{"name":"Первинна дитяча пухлина серця","synonyms":["Пухлина серця у дитини","Пухлина серця у дитини"],"definition":"Cardiac tumours are benign or malignant neoplasms arising primarily in the inner lining, muscle layer, or the surrounding pericardium of the heart. They can be primary or metastatic."},"zh":{"name":"原发性小儿心脏肿瘤","synonyms":["儿童心脏肿瘤"]},"tr":{"name":"Primer pediatrik kalp tümörü","synonyms":["Çocuklarda kalp tümörü","Çocuklarda kardiyak tümör"]}},"xrefs":[{"source":"ICD-10","code":"C38.0","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-10","code":"D15.1","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"2F01","qualifier":"NTBT","icd_relation":"index","validated":true,"icd11_uri":"2122837474"},{"source":"MONDO","code":"0019494","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C4274356","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":250908,"name":"Rare neoplastic disease"},"parents":[{"orpha":168194,"name":"Rare cardiac tumor","classifications":[146,202]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":["Childhood"],"prevalence":[{"type":"Point prevalence","qualification":"Class only","class":"Unknown","value":0.0,"area":"Worldwide","status":"Not yet validated","source":"ORPHANET"}],"phenotypes":null}