ORPHA:86850
Myeloid sarcoma
Synonyms: Chloroma · Extramedullary myeloid tumor · Granulocytic sarcoma
- Type
- Disease
- Group
- Disorder
- Inheritance
- Not applicable
- Age of onset
- All ages
- Status
- active
Myeloid sarcoma is a rare solid tumor of the myelogenous cells occurring in an extramedullary site.
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Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Myeloid sarcoma | Chloroma · Extramedullary myeloid tumor · Granulocytic sarcoma |
| fr | Sarcome myéloïde | Chlorome · Sarcome granulocytaire · Tumeur myéloïde extramédullaire |
| de | Myeloisches Sarkom | Chlorom · Myeloides Sarkom · Myelosarkom · Sarkom, granulozytäres · Tumor, extramedullärer myeloischer |
| es | Sarcoma mieloide | Cloroma · Sarcoma granulocítico · Tumor mieloide extramedular |
| it | Sarcoma mieloide | Cloroma · Sarcoma granulocitico · Tumore mieloide extramidollare |
| nl | Myeloïd sarcoom | Chloroom · Extramedullaire myeloïde tumor · Granulocytair sarcoom |
| pt | Sarcoma mielóide | |
| pl | Mięsak mieloidalny | Chloroma · Mięsak granulocytarny · Pozaszpikowy guz mieloidalny |
| cs | Myeloidní sarkom | Chlorom · Extramedulární myeloidní nádor · Granulocystický sarkom |
| uk | Мієлоїдна саркома | Хлорома · Екстрамедулярна мієлоїдна пухлина · Гранулоцитарна саркома |
| zh | 髓系肉瘤 | 髓外髓样肿瘤 |
| tr | Miyeloid sarkom | Klorom · Granülositik sarkom · Ekstramedüller miyeloid tümör |
Definition in:
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Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | C92.3 | NTBT | attributed | validated |
| ICD-11 | 2A60.39 | E | specific | validated |
| MONDO | 0006861 | E | validated | |
| MeSH | D023981 | E | validated | |
| UMLS | C4721505 | E | validated | |
| GARD | 12763 | E | validated | |
| MedDRA | 10008583 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
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Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:167714Unclassified acute myeloid leukemia
rare hematological diseases; rare neoplastic diseases; rare transplant-related disorders
No children.
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Genes
0 directOrphanet records no gene directly on this code.
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Prevalence and incidence
2 records| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Point prevalence | Unknown | — | Worldwide | Class only | Not yet validated | ORPHANET |
| Annual incidence | <1 / 1 000 000 | 0.02 / 100 000 | Europe | Value and class | Validated | RARECARE surveillance of rare cancers in Europe[OTHER] |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
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HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
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Sources for this card
- Orphanet page: orpha.net/en/disease/detail/86850
- This record as JSON: /data/d/86850.json