{"orpha":86850,"name":"Myeloid sarcoma","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":["Chloroma","Extramedullary myeloid tumor","Granulocytic sarcoma"],"definition":"Myeloid sarcoma is a rare solid tumor of the myelogenous cells occurring in an extramedullary site.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-86850/","orphanet_url":"https://www.orpha.net/en/disease/detail/86850","names":{"fr":{"name":"Sarcome myéloïde","synonyms":["Chlorome","Sarcome granulocytaire","Tumeur myéloïde extramédullaire"],"definition":"Le sarcome myéloïde est une tumeur solide rare des cellules myéloïdes extramédullaires."},"de":{"name":"Myeloisches Sarkom","synonyms":["Chlorom","Myeloides Sarkom","Myelosarkom","Sarkom, granulozytäres","Tumor, extramedullärer myeloischer"],"definition":"Das Myeloische Sarkom ist ein solider Tumor von Knochenmarkzellen, der außerhalb des Knochenmarks entsteht."},"es":{"name":"Sarcoma mieloide","synonyms":["Cloroma","Sarcoma granulocítico","Tumor mieloide extramedular"],"definition":"Es un tumor sólido poco frecuente de las células mieloides que se presenta en un sitio extramedular."},"it":{"name":"Sarcoma mieloide","synonyms":["Cloroma","Sarcoma granulocitico","Tumore mieloide extramidollare"]},"nl":{"name":"Myeloïd sarcoom","synonyms":["Chloroom","Extramedullaire myeloïde tumor","Granulocytair sarcoom"],"definition":"Myeloïd sarcoom is een zeldzame solide tumor van myeloïde cellen die optreedt op een extramedullaire locatie."},"pt":{"name":"Sarcoma mielóide"},"pl":{"name":"Mięsak mieloidalny","synonyms":["Chloroma","Mięsak granulocytarny","Pozaszpikowy guz mieloidalny"]},"cs":{"name":"Myeloidní sarkom","synonyms":["Chlorom","Extramedulární myeloidní nádor","Granulocystický sarkom"]},"uk":{"name":"Мієлоїдна саркома","synonyms":["Хлорома","Екстрамедулярна мієлоїдна пухлина","Гранулоцитарна саркома"],"definition":"Myeloid sarcoma is a rare solid tumor of the myelogenous cells occurring in an extramedullary site."},"zh":{"name":"髓系肉瘤","synonyms":["髓外髓样肿瘤"]},"tr":{"name":"Miyeloid sarkom","synonyms":["Klorom","Granülositik sarkom","Ekstramedüller miyeloid tümör"]}},"xrefs":[{"source":"ICD-10","code":"C92.3","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"2A60.39","qualifier":"E","icd_relation":"specific","validated":true,"icd11_uri":"1988933820"},{"source":"MONDO","code":"0006861","qualifier":"E","icd_relation":null,"validated":true},{"source":"MeSH","code":"D023981","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C4721505","qualifier":"E","icd_relation":null,"validated":true},{"source":"GARD","code":"12763","qualifier":"E","icd_relation":null,"validated":true},{"source":"MedDRA","code":"10008583","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":250908,"name":"Rare neoplastic disease"},"parents":[{"orpha":167714,"name":"Unclassified acute myeloid leukemia","classifications":[194,202,233]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":["All ages"],"prevalence":[{"type":"Point prevalence","qualification":"Class only","class":"Unknown","value":0.0,"area":"Worldwide","status":"Not yet validated","source":"ORPHANET"},{"type":"Annual incidence","qualification":"Value and class","class":"<1 / 1 000 000","value":0.02,"area":"Europe","status":"Validated","source":"RARECARE surveillance of rare cancers in Europe[OTHER]"}],"phenotypes":null}