ORPHA:84271
Sporadic idiopathic steroid-resistant nephrotic syndrome
inactive · moved to ORPHA:656Hereditary steroid-resistant nephrotic syndrome
Synonyms: Sporadic idiopathic nephrosis
- Type
- Clinical syndrome
- Group
- Disorder
- Status
- inactive
- Flag
- Deprecated entity
This entity has been excluded from the Orphanet nomenclature of rare diseases and moved to Genetic steroid-resistant nephrotic syndrome
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Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Sporadic idiopathic steroid-resistant nephrotic syndrome | Sporadic idiopathic nephrosis |
| fr | Syndrome néphrotique idiopathique sporadique corticorésistant | Néphrose idiopathique sporadique |
| de | Nephrotisches Syndrom, idiopathisches steroid-resistentes, sporadisches | Nephrose, idiopathische, sporadische Form |
| es | Síndrome nefrótico idiopático resistente a esteroides esporádico | |
| it | Sindrome nefrosica idiopatica sporadica steroido-resistente | Nefrosi idiopatica, forma sporadica |
| nl | Sporadisch idiopathisch steroïdresistent nefrotisch syndroom | Sporadische idiopathische nefrose |
| pt | Síndrome nefrótico corticorresistente idiopático esporádico | Nefrose idiopática esporádica |
| pl | Sporadyczny idiopatyczny steroidooporny zespół nerczycowy | Sporadyczna idiopatyczna nefroza |
| cs | Sporadický idiopatický steroid-rezistentní nefrotický syndrom | Sporadická idiopatická nefróza |
| uk | Спорадичний ідіопатичний стероїдорезистентний нефротичний синдром | Спорадичний ідіопатичний нефроз |
| zh | 偶发性特发性激素抵抗型肾病综合征 | 散发性特发性肾病 |
| tr | Sporadik idiyopatik steroide dirençli nefrotik sendrom | Sporadik idiyopatik nefroz |
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Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | N04.1 | NTBT | attributed | validated |
| ICD-10 | N04.3 | NTBT | attributed | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
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Classification
Not placed in any Orphanet classification in this release.
No children.
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Genes
0 directOrphanet records no gene directly on this code.
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Prevalence and incidence
0 recordsNo prevalence record in this release.
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HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
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Sources for this card
- Orphanet page: orpha.net/en/disease/detail/84271
- This record as JSON: /data/d/84271.json