raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:84271

Sporadic idiopathic steroid-resistant nephrotic syndrome

inactive · moved to ORPHA:656Hereditary steroid-resistant nephrotic syndrome

Synonyms: Sporadic idiopathic nephrosis

Type
Clinical syndrome
Group
Disorder
Status
inactive
Flag
Deprecated entity

This entity has been excluded from the Orphanet nomenclature of rare diseases and moved to Genetic steroid-resistant nephrotic syndrome

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enSporadic idiopathic steroid-resistant nephrotic syndromeSporadic idiopathic nephrosis
frSyndrome néphrotique idiopathique sporadique corticorésistantNéphrose idiopathique sporadique
deNephrotisches Syndrom, idiopathisches steroid-resistentes, sporadischesNephrose, idiopathische, sporadische Form
esSíndrome nefrótico idiopático resistente a esteroides esporádico
itSindrome nefrosica idiopatica sporadica steroido-resistenteNefrosi idiopatica, forma sporadica
nlSporadisch idiopathisch steroïdresistent nefrotisch syndroomSporadische idiopathische nefrose
ptSíndrome nefrótico corticorresistente idiopático esporádicoNefrose idiopática esporádica
plSporadyczny idiopatyczny steroidooporny zespół nerczycowySporadyczna idiopatyczna nefroza
csSporadický idiopatický steroid-rezistentní nefrotický syndromSporadická idiopatická nefróza
ukСпорадичний ідіопатичний стероїдорезистентний нефротичний синдромСпорадичний ідіопатичний нефроз
zh偶发性特发性激素抵抗型肾病综合征散发性特发性肾病
trSporadik idiyopatik steroide dirençli nefrotik sendromSporadik idiyopatik nefroz
2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-10N04.1NTBTattributedvalidated
ICD-10N04.3NTBTattributedvalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Not placed in any Orphanet classification in this release.

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card