{"orpha":84271,"name":"Sporadic idiopathic steroid-resistant nephrotic syndrome","type":"Clinical syndrome","group":"Disorder","status":"inactive","flags":["Deprecated entity"],"synonyms":["Sporadic idiopathic nephrosis"],"definition":null,"note":"This entity has been excluded from the Orphanet nomenclature of rare diseases and moved to Genetic steroid-resistant nephrotic syndrome","url":"https://raremap.alftech.space/d/ORPHA-84271/","orphanet_url":"https://www.orpha.net/en/disease/detail/84271","names":{"fr":{"name":"Syndrome néphrotique idiopathique sporadique corticorésistant","synonyms":["Néphrose idiopathique sporadique"]},"de":{"name":"Nephrotisches Syndrom, idiopathisches steroid-resistentes, sporadisches","synonyms":["Nephrose, idiopathische, sporadische Form"]},"es":{"name":"Síndrome nefrótico idiopático resistente a esteroides esporádico"},"it":{"name":"Sindrome nefrosica idiopatica sporadica steroido-resistente","synonyms":["Nefrosi idiopatica, forma sporadica"]},"nl":{"name":"Sporadisch idiopathisch steroïdresistent nefrotisch syndroom","synonyms":["Sporadische idiopathische nefrose"]},"pt":{"name":"Síndrome nefrótico corticorresistente idiopático esporádico","synonyms":["Nefrose idiopática esporádica"]},"pl":{"name":"Sporadyczny idiopatyczny steroidooporny zespół nerczycowy","synonyms":["Sporadyczna idiopatyczna nefroza"]},"cs":{"name":"Sporadický idiopatický steroid-rezistentní nefrotický syndrom","synonyms":["Sporadická idiopatická nefróza"]},"uk":{"name":"Спорадичний ідіопатичний стероїдорезистентний нефротичний синдром","synonyms":["Спорадичний ідіопатичний нефроз"]},"zh":{"name":"偶发性特发性激素抵抗型肾病综合征","synonyms":["散发性特发性肾病"]},"tr":{"name":"Sporadik idiyopatik steroide dirençli nefrotik sendrom","synonyms":["Sporadik idiyopatik nefroz"]}},"xrefs":[{"source":"ICD-10","code":"N04.1","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-10","code":"N04.3","qualifier":"NTBT","icd_relation":"attributed","validated":true}],"associations":[{"type":"Moved to","orpha":656,"name":"Hereditary steroid-resistant nephrotic syndrome"}],"incoming_associations":[],"preferential_parent":null,"parents":[],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":[],"prevalence":[],"phenotypes":null}