raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:83593

Western equine encephalitis

Synonyms: Western equine encephalomyelitis

Type
Disease
Group
Disorder
Inheritance
Not applicable
Age of onset
All ages
Status
active

An acute arboviral infection caused by an <i>alphavirus</i> of the <i>Togaviridae</i> family transmitted by an infected mosquito, that more frequently affects children and that is characterized by the presence of mild flu-like symptoms (fever, chills, headache, nausea, vomiting, and anorexia) but that can progress to weakness, altered mental status, photophobia, mental confusion, seizures, somnolence, coma and/or even death. The disease can leave neurological sequelae, mainly in infants and children, such as seizures, spasticity or behavioral disorders.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enWestern equine encephalitisWestern equine encephalomyelitis
frEncéphalite équine de l'ouestEncéphalomyélite équine de l'ouest
deWestliche PferdeenzephalitisWestern-Equine-Encephalitis
esEncefalitis equina occidentalEncefalomielitis equina occidental
itEncefalite equina dell'OvestEncefalomielite equina dell'Ovest
nlWesterse paardenencefalitisWesterse equine encefalitis · Westerse paardenencefalomyelitis
ptEncefalite equina ocidentalEncefalomielite equina ocidental
plZachodnie końskie zapalenie mózguZachodnie końskie zapalenie mózgu i opon mózgowych
csZápadní koňská encefalitidaZápadní koňská encefalomyelitida
ukЗахідний кінський енцефалітЗахідний енцефаломієліт коней
zh西方马脑炎西部马脑脊髓炎
trBatı at ensefalitiBatı at ensefalomiyeliti

Definition in:

2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-10A83.1NTBTattributedvalidated
ICD-111C83Especificvalidated
MONDO0019380Evalidated
MeSHD020241Evalidated
UMLSC0153064Evalidated
GARD7888Evalidated
MedDRA10014614Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

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Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (2):

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

2 records
TypeClassValueAreaQualificationValidationSource
Annual incidence<1 / 1 000 0000.02 / 100 000United StatesValue and classValidatedCenter for Diseases Control and Prevention[OTHER]
Point prevalence1-9 / 1 000 000—EuropeClass onlyNot yet validatedORPHANET

Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

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Sources for this card