raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:83483

La Crosse encephalitis

Synonyms: Californian encephalitis

Type
Disease
Group
Disorder
Inheritance
Not applicable
Age of onset
All ages
Status
active

An acute arboviral infection caused by the <i>La Crosse bunyavirus</i> transmitted by an infected mosquito, usually observed in infants, children or adolescents (6 months to 16 years), and characterized by the onset of flulike symptoms such as fever, chills, nausea, vomiting, headache, and abdominal pain, followed by the onset of encephalitis characterized by somnolence, obtundation, and even seizures, focal neurologic signs (asymmetrical reflexes or Babinski signs), paralysis or even coma. CE can leave sequelae such as residual epilepsy and neurocognitive deficits.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enLa Crosse encephalitisCalifornian encephalitis
frEncéphalite de La CrosseEncéphalite de Californie
deKalifornische Enzephalitis
esEncefalitis de La CrosseEncefalitis californiana
itEncefalite di La CrosseEncefalite californiana
nlLa Crosse-encefalitisCalifornië-encefalitis
ptEncefalite da Califórnia
plZapalenie mózgu La CrosseKalifornijskie zapalenie mózgu
csLa Crossova encefalitidaKalifornská encefalitida
ukЕнцефаліт Ла-КроссаКаліфорнійський енцефаліт
zh大地病毒脑炎加利福尼亚脑炎
trLa Crosse ensefalitiKaliforniya ensefaliti

Definition in:

2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-10A83.5NTBTattributedvalidated
ICD-111C8DNTBTindexvalidated
MONDO0019378Evalidated
MeSHD004670Evalidated
UMLSC0276379Evalidated
GARD10925Evalidated
MedDRA10014584Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

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Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (2):

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

2 records
TypeClassValueAreaQualificationValidationSource
Annual incidence1-9 / 100 0001.91 / 100 000CanadaValue and classValidatedCanada Public Health Agency[OTHER]
Point prevalenceUnknown—WorldwideClass onlyNot yet validatedORPHANET

Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.

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HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

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Sources for this card