raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:83476

West-Nile encephalitis

Synonyms: West-Nile fever

Type
Disease
Group
Disorder
Inheritance
Not applicable
Age of onset
All ages
Status
active

An acute arboviral infection caused by a virus of the <i>Flaviviridae</i> family transmitted by an infected mosquito, that is asymptomatic in the majority of cases but that can present in rare occasions with mild flulike symptoms such as low-grade fever, arthralgia, myalgia, and/or rash, or with neurologic manifestations including meningitis, encephalitis with mental confusion or disorientation, tremors and acute flaccid paralysis/poliomyelitis.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enWest-Nile encephalitisWest-Nile fever
frEncéphalite West-NileFièvre West-Nile
deWest-Nil-EnzephalitisWest-Nil-Fieber
esEncefalitis del Nilo occidentalFiebre del Nilo occidental
itEncefalite del Nilo occidentaleFebbre del Nilo occidentale
nlWest-Nijl-encefalitisWest-Nijl-koorts · Westnijlkoorts
ptEncefalia do Oeste do NiloFebre do Oeste do Nilo
plZapalenie mózgu Zachodniego NiluGorączka Zachodniego Nilu
csZápadonilská encefalitidaZápadonilská horečka
ukЕнцефаліт Західного НілуЛихоманка Західного Нілу
zh西尼罗脑炎西尼罗热
trBatı Nil ensefalitiBatı-Nil ateşi

Definition in:

2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
OMIM610379BTNTvalidated
ICD-10A92.3NTBTattributedvalidated
ICD-111C80NTBTindexvalidated
MONDO0019376Evalidated
MeSHD014901Evalidated
UMLSC0751583Evalidated
GARD9959Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (2):

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

9 records
TypeClassValueAreaQualificationValidationSource
Point prevalence1-9 / 1 000 0000.92 / 100 000United StatesValue and classValidated23013055[PMID]_Center for Diseases Control and Prevention 2012[OTHER]
Point prevalenceUnknown—WorldwideClass onlyNot yet validatedORPHANET
Annual incidence<1 / 1 000 0000.036 / 100 000EuropeValue and classValidatedEuropean Centre for Disease prevention and Control 2011-2015[OTHER]
Annual incidence1-9 / 1 000 0000.12 / 100 000RomaniaValue and classValidatedEuropean Centre for Disease prevention and Control 2011-2015[OTHER]
Annual incidence<1 / 1 000 0000.02 / 100 000AustriaValue and classValidatedEuropean Centre for Disease prevention and Control 2011-2015[OTHER]
Annual incidence1-9 / 1 000 0000.17 / 100 000CroatiaValue and classValidatedEuropean Centre for Disease prevention and Control 2012-2015[OTHER]
Annual incidence1-9 / 1 000 0000.66 / 100 000GreeceValue and classValidatedEuropean Centre for Disease prevention and Control 2011-2015[OTHER]
Annual incidence1-9 / 1 000 0000.16 / 100 000HungaryValue and classValidatedEuropean Centre for Disease prevention and Control 2011-2015[OTHER]
Annual incidence<1 / 1 000 0000.07 / 100 000ItalyValue and classValidatedEuropean Centre for Disease prevention and Control 2011-2013[OTHER]

Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card