raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:83317

Scrub typhus

Synonyms: Tsutsugamushi disease · Tsutsugamushi fever

Type
Disease
Group
Disorder
Age of onset
All ages
Status
active

Scrub typhus is a rare dust mite-borne infectious disease caused by the <i>Orientia tsutsugamushi</i> bacterium and characterized clinically by an eruptive fever which is potentially serious.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enScrub typhusTsutsugamushi disease · Tsutsugamushi fever
frTyphus des broussaillesFièvre de Tsutsugamushi · Fièvre fluviale du Japon · Maladie de Tsutsugamushi
deScrub-TyphusTsutsugamushi-Fieber · Tsutsugamushi-Krankheit
esTifus de las malezasEnfermedad de Tsutsugamushi · Fiebre de Tsutsugamushi
itTifo da acariFebbre di Tsutsugamushi · Malattia di Tsutsugamushi
nlScrubtyfusInfectie door Orientia tsutsugamushi · Tsutsugamushi-koorts · Tsutsugamushi-ziekte
ptTifo dos arbustosDoença de Tsutsugamushi · Febre de Tsutsugamushi
plJapońska gorączka rzecznaChoroba tsutsugamushi · Gorączka tsutsugamushi
csKřovinný tyfusNemoc tsutsugamushi · Horečka tsutsugamushi · Japonská říční horečka
ukСкрабовий висипний тифХвороба Цуцугамуші · Лихоманка Цуцугамуші
zh恙虫热斑疹伤寒恙虫病
trScrub tifüsTsutsugamushi ateşi · Tsutsugamushi hastalığı

Definition in:

2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-10A75.3Especificvalidated
ICD-111C30.3Especificvalidated
MONDO0019365Evalidated
MeSHD012612Evalidated
UMLSC0036472Evalidated
MedDRA10039766Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

3 records
TypeClassValueAreaQualificationValidationSource
Point prevalence1-9 / 100 0007.2 / 100 000Korea, Republic ofValue and classValidated18362409[PMID]
Point prevalence1-9 / 1 000 0000.3 / 100 000JapanValue and classValidated18362409[PMID]
Point prevalenceUnknown—WorldwideClass onlyNot yet validatedORPHANET

Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.

6

HPO phenotypes

27 annotations · validated 2016-06-01
HPOTerm (as annotated by Orphanet)Diagnostic
Very frequent (99-80%)
HP:0012735Cough
HP:0001945Fever
HP:0000975Hyperhidrosis
HP:0001254Lethargy
HP:0003326Myalgia
HP:0004372Reduced consciousness
HP:0000988Skin rash
Frequent (79-30%)
HP:0002027Abdominal pain
HP:0012122Anterior uveitis
HP:0100758Gangrene
HP:0002315Headache
HP:0002615Hypotension
HP:0002716Lymphadenopathy
HP:0012733Macule
HP:0002017Nausea and vomiting
HP:0000613Photophobia
Occasional (29-5%)
HP:0001892Abnormal bleeding
HP:0000708Atypical behavior
HP:0002094Dyspnea
HP:0002383Infectious encephalitis
HP:0001287Meningitis
HP:0012819Myocarditis
HP:0000083Renal insufficiency
HP:0002091Restrictive ventilatory defect
HP:0001250Seizure
HP:0001744Splenomegaly
HP:0001337Tremor

Run the differential on the 7 obligate / very frequent terms

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Sources for this card