raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:770

Rabies

Type
Disease
Group
Disorder
Inheritance
Not applicable
Age of onset
All ages
Status
active

Rabies is a viral zoonosis leading to a fatal encephalopathy if not treated.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enRabies
frRage
deTollwutRabies
esRabia
itRabbia
nlRabiësHondsdolheid
ptRaiva
plWścieklizna
csVzteklinaRabies · Lyssa
ukСказ
zh狂犬病
trKuduz

Definition in:

2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-10A82.0BTNTspecificvalidated
ICD-10A82.1BTNTspecificvalidated
ICD-10A82.9BTNTspecificvalidated
ICD-111C82Especificvalidated
MONDO0019173Evalidated
MeSHD011818Evalidated
UMLSC0034494Evalidated
GARD7516Evalidated
MedDRA10037742Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (2):

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

3 records
TypeClassValueAreaQualificationValidationSource
Point prevalence1-9 / 1 000 000—EuropeClass onlyValidated[EXPERT]
Point prevalence<1 / 1 000 000—United StatesClass onlyNot yet validated22699971[PMID]
Annual incidence<1 / 1 000 000—EuropeClass onlyValidatedEuropean Centre for Disease prevention and Control 2017[OTHER]

Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.

6

HPO phenotypes

19 annotations · validated 2016-06-01
HPOTerm (as annotated by Orphanet)Diagnostic
Very frequent (99-80%)
HP:0002039Anorexia
HP:0000739Anxiety
HP:0007018Attention deficit hyperactivity disorder
HP:0000708Atypical behavior
HP:0000716Depression
HP:0002014Diarrhea
HP:0003781Excessive salivation
HP:0001945Fever
HP:0000738Hallucinations
HP:0100785Insomnia
HP:0002076Migraine
HP:0002017Nausea and vomiting
HP:0003401Paresthesia
HP:0100776Recurrent pharyngitis
HP:0001604Vocal cord paresis
Frequent (79-30%)
HP:0100021Cerebral palsy
Occasional (29-5%)
HP:0004372Reduced consciousness
HP:0001250Seizure
HP:0001645Sudden cardiac death

Run the differential on the 12 obligate / very frequent terms

7

Sources for this card