raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:730276

Primary autoimmune ear disease

Synonyms: Primary autoimmune sensorineural hearing loss · Immune mediated inner ear disease type 1 · IMIED type 1

Type
Disease
Group
Disorder
Inheritance
Not applicable
Status
active

Orphadata ships no English definition for this code.

1

Names in Orphadata languages

9 of 12 languages
LangNameSynonyms
enPrimary autoimmune ear diseasePrimary autoimmune sensorineural hearing loss · Immune mediated inner ear disease type 1 · IMIED type 1
frMaladie auto-immune de l'oreille internePerte auditive neurosensorielle auto-immune primaire · MAOI primaire
dePrimäre Autoimmunerkrankungen des InnenohresIMIED Typ 1 · Immunvermittelte Innenohrerkrankung Typ 1 · Primärer autoimmuner sensorineuraler Hörverlust
esEnfermedad autoinmune primaria del oídoEnfermedad inmunomediada del oído interno tipo 1 · Hipoacusia neurosensorial autoinmune primaria · IMIED tipo 1
itMalattia autoimmune primitiva dell'orecchioIMIED tipo 1 · Malattia dell'orecchio interno immuno-mediata tipo 1 · Sordità neurosensoriale autoimmune primitiva
nlPrimaire auto-immune oorziekteIMIED type 1 · Immuungemedieerde aandoening van binnenoor type 1 · Primair auto-immuun sensorineuraal gehoorverlies
ptPrimary autoimmune ear disease
plPrimary autoimmune ear disease= en
csPrimary autoimmune ear disease= en
2

Cross-references

qualifier = Orphanet mapping relation

No cross-references in this release.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card